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Three-dimensional echocardiographic left ventricular strain analysis in Fabry disease: correlation with heart failure severity, myocardial scar, and impact on long-term prognosis
AIMS: Fabry disease (FD) is a multisystemic lysosomal storage disorder caused by a defect in the alpha-galactosidase A gene that manifests as a phenocopy of hypertrophic cardiomyopathy. We assessed the echocardiographic 3D left ventricular (LV) strain of patients with FD in relation to heart failure...
Autores principales: | Marek, Josef, Chocholová, Barbora, Rob, Daniel, Paleček, Tomáš, Mašek, Martin, Dostálová, Gabriela, Linhart, Aleš |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Oxford University Press
2023
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10667034/ https://www.ncbi.nlm.nih.gov/pubmed/37309820 http://dx.doi.org/10.1093/ehjci/jead121 |
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