Cargando…

Editorial: Real-world experience with CFTR modulator therapy

Detalles Bibliográficos
Autores principales:	Tümmler, Burkhard, Burgel, Pierre-Régis
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Frontiers Media S.A. 2023
Materias:	Pharmacology
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10682817/ https://www.ncbi.nlm.nih.gov/pubmed/38035017 http://dx.doi.org/10.3389/fphar.2023.1331829

Ejemplares similares

Post-approval studies with the CFTR modulators Elexacaftor-Tezacaftor—Ivacaftor
por: Tümmler, Burkhard
Publicado: (2023)

CFTR Modulators in People with Cystic Fibrosis: Real-World Evidence in France
por: Regard, Lucile, et al.
Publicado: (2022)

Real-world disparities and ethical considerations with access to CFTR modulator drugs: Mind the gap!
por: Zampoli, M., et al.
Publicado: (2023)

Differential effects of ELX/TEZ/IVA on organ-specific CFTR function in two patients with the rare CFTR splice mutations c.273+1G>A and c.165-2A>G
por: Pallenberg, Sophia T., et al.
Publicado: (2023)

Real-life impact of highly effective CFTR modulator therapy in children with cystic fibrosis
por: Olivier, Margarete, et al.
Publicado: (2023)

Role of inhaled antibiotics in the era of highly effective CFTR modulators
por: Elborn, J. Stuart, et al.
Publicado: (2023)

Airway Epithelial Inflammation In Vitro Augments the Rescue of Mutant CFTR by Current CFTR Modulator Therapies
por: Gentzsch, Martina, et al.
Publicado: (2021)

Gene Therapy: A Possible Alternative to CFTR Modulators?
por: Mercier, J., et al.
Publicado: (2021)

Dual CFTR modulator therapy efficacy in the real world: lessons for the future
por: Dittrich, Anna-Maria, et al.
Publicado: (2022)

Puzzle resolved: CFTR mediates chloride homeostasis by segregating absorption and secretion to different cell types
por: Tümmler, Burkhard
Publicado: (2023)

Molecular Mechanism of Action of Trimethylangelicin Derivatives as CFTR Modulators
por: Laselva, Onofrio, et al.
Publicado: (2018)

The effect of CFTR modulators on structural lung disease in cystic fibrosis
por: Mok, L. Clara, et al.
Publicado: (2023)

CFTR Modulators: Shedding Light on Precision Medicine for Cystic Fibrosis
por: Lopes-Pacheco, Miquéias
Publicado: (2016)

Editorial: Big Data, Pharmacogenomics and Real-World Research in Pharmacology
por: Wei, James Cheng-Chung, et al.
Publicado: (2020)

Weight increase in people with cystic fibrosis on CFTR modulator therapy is mainly due to increase in fat mass
por: Mouzaki, Marialena, et al.
Publicado: (2023)

CFTR Modulator Therapy Enhances Peripheral Blood Monocyte Contributions to Immune Responses in People With Cystic Fibrosis
por: Hisert, Katherine B., et al.
Publicado: (2020)

CFTR Modulators: The Changing Face of Cystic Fibrosis in the Era of Precision Medicine
por: Lopes-Pacheco, Miquéias
Publicado: (2020)

Development of CFTR Structure
por: Patrick, Anna E., et al.
Publicado: (2012)

New therapies for people with CF in the CFTR modulator world
por: Wainwright, Claire E
Publicado: (2020)

Editorial: The use of real world data for regulatory purposes in the rare diseases setting
por: Giannuzzi, Viviana, et al.
Publicado: (2022)

Investigating the Implications of CFTR Exon Skipping Using a Cftr Exon 9 Deleted Mouse Model
por: Martinovich, Kelly M., et al.
Publicado: (2022)

Pharmacological Correctors of Mutant CFTR Mistrafficking
por: Pedemonte, Nicoletta, et al.
Publicado: (2012)

Mechanisms of CFTR Folding at the Endoplasmic Reticulum
por: Kim, Soo Jung, et al.
Publicado: (2012)

Identification and Characterization of Novel CFTR Potentiators
por: Gees, Maarten, et al.
Publicado: (2018)

Treatment With LAU-7b Complements CFTR Modulator Therapy by Improving Lung Physiology and Normalizing Lipid Imbalance Associated With CF Lung Disease
por: Centorame, Amanda, et al.
Publicado: (2022)

Real-World Safety of CFTR Modulators in the Treatment of Cystic Fibrosis: A Systematic Review
por: Dagenais, Renée V. E., et al.
Publicado: (2020)

CFTR and Ca(2+) Signaling in Cystic Fibrosis
por: Antigny, Fabrice, et al.
Publicado: (2011)

Strategies to circumvent the CFTR defect in cystic fibrosis
por: Becq, Frédéric, et al.
Publicado: (2013)

Comprehensive Analysis of Chemical Structures That Have Been Tested as CFTR Activating Substances in a Publicly Available Database CandActCFTR
por: Nietert, Manuel Manfred, et al.
Publicado: (2021)

Identification of GLPG/ABBV-2737, a Novel Class of Corrector, Which Exerts Functional Synergy With Other CFTR Modulators
por: de Wilde, Gert, et al.
Publicado: (2019)

Single-Dose Lentiviral Mediated Gene Therapy Recovers CFTR Function in Cystic Fibrosis Knockout Rats
por: Reyne, Nicole, et al.
Publicado: (2021)

Molecular Chaperones as Targets to Circumvent the CFTR Defect in Cystic Fibrosis
por: Chanoux, Rebecca A., et al.
Publicado: (2012)

Allicin Facilitates Airway Surface Liquid Hydration by Activation of CFTR
por: Qiu, Zhuo-Er, et al.
Publicado: (2022)

Proliferative activity of antigen-specific CD154+ T cells against bacterial and fungal respiratory pathogens in cystic fibrosis decreases after initiation of highly effective CFTR modulator therapy
por: Eschenhagen, Patience N., et al.
Publicado: (2023)

Effectiveness and safety of Lacosamide therapy for children with focal epilepsy: a real world study
por: Yang, Chunsong, et al.
Publicado: (2023)

An association study on contrasting cystic fibrosis endophenotypes recognizes KRT8 but not KRT18 as a modifier of cystic fibrosis disease severity and CFTR mediated residual chloride secretion
por: Stanke, Frauke, et al.
Publicado: (2011)

Instability of the insertional mutation in Cftr(TgH(neoim)Hgu )cystic fibrosis mouse model
por: Charizopoulou, Nikoletta, et al.
Publicado: (2004)

Stimulation of Airway and Intestinal Mucosal Secretion by Natural Coumarin CFTR Activators
por: Yang, Hong, et al.
Publicado: (2011)

Recent Progress in CFTR Interactome Mapping and Its Importance for Cystic Fibrosis
por: Lim, Sang Hyun, et al.
Publicado: (2018)

Network Biology Identifies Novel Regulators of CFTR Trafficking and Membrane Stability
por: Loureiro, Cláudia Almeida, et al.
Publicado: (2019)

Cannot write session to /tmp/vufind_sessions/sess_6h01e306au6n8t1652t9ns5ve3