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Nutritional status of adults with phenylketonuria on pegvaliase: A 15-month prospective study

BACKGROUND: Pegvaliase has allowed many adults with phenylketonuria (PKU) to achieve acceptable blood Phe control while eating an unrestricted diet. However, little is known about potential differences in nutritional status and eating behaviors after transitioning from a phenylalanine (Phe)-restrict...

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Detalles Bibliográficos
Autores principales:	Viau, Krista, Martell, Leslie, Wessel, Ann, Rohr, Fran, Hollander, Suzanne, Putman, Melissa S., Sacharow, Stephanie
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Elsevier 2023
Materias:	Research Paper
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10694747/ http://dx.doi.org/10.1016/j.ymgmr.2023.101015

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