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Deficiency in Cardiac Dystrophin Affects the Abundance of the α-/β-Dystroglycan Complex
Although Duchenne muscular dystrophy is primarily categorised as a skeletal muscle disease, deficiency in the membrane cytoskeletal protein dystrophin also affects the heart. The central transsarcolemmal linker between the actin membrane cytoskeleton and the extracellular matrix is represented by th...
Autores principales: | Lohan, James, Culligan, Kevin, Ohlendieck, Kay |
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Formato: | Texto |
Lenguaje: | English |
Publicado: |
Hindawi Publishing Corporation
2005
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC1138265/ https://www.ncbi.nlm.nih.gov/pubmed/15689636 http://dx.doi.org/10.1155/S111072430440103X |
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