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A large left ventricular pseudoaneurysm in Behçet's disease: a case report

BACKGROUND: Behçet's disease is a collagen-vascular disease most commonly seen in Asia and Mediterranean area. Different organs and systems including cardiovascular system could be involved. Pseudoaneurysm is the most common form of arterial involvement in Behçet's disease; however, cardia...

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Autores principales: Marashi, Seyed Mojtaba, Eghtesadi-Araghi, Payam, Mandegar, Mohammad Hussein
Formato: Texto
Lenguaje:English
Publicado: BioMed Central 2005
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC1181820/
https://www.ncbi.nlm.nih.gov/pubmed/15955242
http://dx.doi.org/10.1186/1471-2482-5-13
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author Marashi, Seyed Mojtaba
Eghtesadi-Araghi, Payam
Mandegar, Mohammad Hussein
author_facet Marashi, Seyed Mojtaba
Eghtesadi-Araghi, Payam
Mandegar, Mohammad Hussein
author_sort Marashi, Seyed Mojtaba
collection PubMed
description BACKGROUND: Behçet's disease is a collagen-vascular disease most commonly seen in Asia and Mediterranean area. Different organs and systems including cardiovascular system could be involved. Pseudoaneurysm is the most common form of arterial involvement in Behçet's disease; however, cardiac pseudoaneurysm is rare. CASE PRESENTATION: A rare case of 13 years old boy with a 4-year history of Behçet's disease with development of a huge left ventricular pseudoaneurysm is reported who had been admitted because of cough, chills, fever, and chest pain. Findings obtained on echocardiography, magnetic resonance imaging, chest computed tomography and coronary angiography confirmed a left ventricular pseudoaneurysm. There was no complication for next 24 months follow up period after surgical treatment. CONCLUSION: Considering its fatality and nonspecific manifestations, one should consider cardiac pseudoaneurysms as a potential risk in any patient with Behçet's disease.
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spelling pubmed-11818202005-07-30 A large left ventricular pseudoaneurysm in Behçet's disease: a case report Marashi, Seyed Mojtaba Eghtesadi-Araghi, Payam Mandegar, Mohammad Hussein BMC Surg Case Report BACKGROUND: Behçet's disease is a collagen-vascular disease most commonly seen in Asia and Mediterranean area. Different organs and systems including cardiovascular system could be involved. Pseudoaneurysm is the most common form of arterial involvement in Behçet's disease; however, cardiac pseudoaneurysm is rare. CASE PRESENTATION: A rare case of 13 years old boy with a 4-year history of Behçet's disease with development of a huge left ventricular pseudoaneurysm is reported who had been admitted because of cough, chills, fever, and chest pain. Findings obtained on echocardiography, magnetic resonance imaging, chest computed tomography and coronary angiography confirmed a left ventricular pseudoaneurysm. There was no complication for next 24 months follow up period after surgical treatment. CONCLUSION: Considering its fatality and nonspecific manifestations, one should consider cardiac pseudoaneurysms as a potential risk in any patient with Behçet's disease. BioMed Central 2005-06-14 /pmc/articles/PMC1181820/ /pubmed/15955242 http://dx.doi.org/10.1186/1471-2482-5-13 Text en Copyright © 2005 Marashi et al; licensee BioMed Central Ltd. http://creativecommons.org/licenses/by/2.0 This is an Open Access article distributed under the terms of the Creative Commons Attribution License ( (http://creativecommons.org/licenses/by/2.0) ), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Marashi, Seyed Mojtaba
Eghtesadi-Araghi, Payam
Mandegar, Mohammad Hussein
A large left ventricular pseudoaneurysm in Behçet's disease: a case report
title A large left ventricular pseudoaneurysm in Behçet's disease: a case report
title_full A large left ventricular pseudoaneurysm in Behçet's disease: a case report
title_fullStr A large left ventricular pseudoaneurysm in Behçet's disease: a case report
title_full_unstemmed A large left ventricular pseudoaneurysm in Behçet's disease: a case report
title_short A large left ventricular pseudoaneurysm in Behçet's disease: a case report
title_sort large left ventricular pseudoaneurysm in behçet's disease: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC1181820/
https://www.ncbi.nlm.nih.gov/pubmed/15955242
http://dx.doi.org/10.1186/1471-2482-5-13
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