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Successful whole lung lavage in pulmonary alveolar proteinosis secondary to lysinuric protein intolerance: a case report
BACKGROUND: Pulmonary alveolar proteinosis (PAP) is a rare disease characterised by accumulation of lipoproteinaceous material within alveoli, occurring in three clinically distinct forms: congenital, acquired and secondary. Among the latter, lysinuric protein intolerance (LPI) is a rare genetic dis...
Autores principales: | Ceruti, Michele, Rodi, Giuseppe, Stella, Giulia M, Adami, Andrea, Bolongaro, Antonia, Baritussio, Aldo, Pozzi, Ernesto, Luisetti, Maurizio |
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Formato: | Texto |
Lenguaje: | English |
Publicado: |
BioMed Central
2007
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC1845139/ https://www.ncbi.nlm.nih.gov/pubmed/17386098 http://dx.doi.org/10.1186/1750-1172-2-14 |
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