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Fibrous dysplasia of the cranial bones: a case report and review of the literature.
Fibrous dysplasia (FD) is a relatively uncommon disorder that affects primarily the cranial region; its occurrence in the cranial base in combination with hindbrain herniation and aneurysmal bone cyst (ABC) constitutes an extremely rare condition. We report a case of polyostotic fibrous dysplasia wi...
Autores principales: | , , , |
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Formato: | Texto |
Lenguaje: | English |
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Yale Journal of Biology and Medicine
2005
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2259144/ https://www.ncbi.nlm.nih.gov/pubmed/16464312 |
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author | Iseri, Pervin K. Efendi, Husnu Demirci, Ali Komsuoglu, Sezer |
author_facet | Iseri, Pervin K. Efendi, Husnu Demirci, Ali Komsuoglu, Sezer |
author_sort | Iseri, Pervin K. |
collection | PubMed |
description | Fibrous dysplasia (FD) is a relatively uncommon disorder that affects primarily the cranial region; its occurrence in the cranial base in combination with hindbrain herniation and aneurysmal bone cyst (ABC) constitutes an extremely rare condition. We report a case of polyostotic fibrous dysplasia with progressive occipital, temporal, and clival involvement. Clinical findings and differential diagnosis with special emphasis on the imaging features were discussed. A small posterior fossa volume has been thought to lead to hind brain herniation. The resultant obstruction to the CSF pathways at the level of the foramen magnum has been implicated in the development and subsequent progression of syringobulbia. |
format | Text |
id | pubmed-2259144 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2005 |
publisher | Yale Journal of Biology and Medicine |
record_format | MEDLINE/PubMed |
spelling | pubmed-22591442008-03-03 Fibrous dysplasia of the cranial bones: a case report and review of the literature. Iseri, Pervin K. Efendi, Husnu Demirci, Ali Komsuoglu, Sezer Yale J Biol Med Research Article Fibrous dysplasia (FD) is a relatively uncommon disorder that affects primarily the cranial region; its occurrence in the cranial base in combination with hindbrain herniation and aneurysmal bone cyst (ABC) constitutes an extremely rare condition. We report a case of polyostotic fibrous dysplasia with progressive occipital, temporal, and clival involvement. Clinical findings and differential diagnosis with special emphasis on the imaging features were discussed. A small posterior fossa volume has been thought to lead to hind brain herniation. The resultant obstruction to the CSF pathways at the level of the foramen magnum has been implicated in the development and subsequent progression of syringobulbia. Yale Journal of Biology and Medicine 2005-05 /pmc/articles/PMC2259144/ /pubmed/16464312 Text en |
spellingShingle | Research Article Iseri, Pervin K. Efendi, Husnu Demirci, Ali Komsuoglu, Sezer Fibrous dysplasia of the cranial bones: a case report and review of the literature. |
title | Fibrous dysplasia of the cranial bones: a case report and review of the literature. |
title_full | Fibrous dysplasia of the cranial bones: a case report and review of the literature. |
title_fullStr | Fibrous dysplasia of the cranial bones: a case report and review of the literature. |
title_full_unstemmed | Fibrous dysplasia of the cranial bones: a case report and review of the literature. |
title_short | Fibrous dysplasia of the cranial bones: a case report and review of the literature. |
title_sort | fibrous dysplasia of the cranial bones: a case report and review of the literature. |
topic | Research Article |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2259144/ https://www.ncbi.nlm.nih.gov/pubmed/16464312 |
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