Cargando…

Lennox gastaut syndrome, review of the literature and a case report

BACKGROUND: Lennox-Gastaut syndrome (LGS) is a severe form of childhood epilepsy that is defined by generalized multiple type seizures, slowness of intellectual growth, and a specific EEG disturbance. Children affected might previously have infantile spasms or underlying brain disorder but etiology...

Descripción completa

Detalles Bibliográficos
Autores principales: Abu Saleh, Tareq, Stephen, Lawrence
Formato: Texto
Lenguaje:English
Publicado: BioMed Central 2008
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2483705/
https://www.ncbi.nlm.nih.gov/pubmed/18541034
http://dx.doi.org/10.1186/1746-160X-4-9
_version_ 1782158058863984640
author Abu Saleh, Tareq
Stephen, Lawrence
author_facet Abu Saleh, Tareq
Stephen, Lawrence
author_sort Abu Saleh, Tareq
collection PubMed
description BACKGROUND: Lennox-Gastaut syndrome (LGS) is a severe form of childhood epilepsy that is defined by generalized multiple type seizures, slowness of intellectual growth, and a specific EEG disturbance. Children affected might previously have infantile spasms or underlying brain disorder but etiology can be idiopathic. In South Africa, the incidence of secondary epilepsy is higher than what is found in developed countries resulting in higher incidence of the disease. LGS seizures are often treatment resistant and the long term prognosis is poor. REPORT: A twenty six year old female, presented with anterior open bite, macroglossia, supragingival as well as subgingival calculus. The gingiva was red, swollen and friable and there was generalized bleeding and localized suppuration. The patient had gingival recession. After periodontal therapy a remarkable improvement in oral health status was noted. CONCLUSION: The clinical findings in LGS included facial deformities, periodontitis and gingival swellings. Interdisciplinary treatment of these patients is fundamental and oral attention is of outstanding importance. Non-surgical periodontal therapy was effective in controlling periodontal disease in the reported case, but prevention of periodontal and dental diseases is preferable for this high-risk group of patients.
format Text
id pubmed-2483705
institution National Center for Biotechnology Information
language English
publishDate 2008
publisher BioMed Central
record_format MEDLINE/PubMed
spelling pubmed-24837052008-07-25 Lennox gastaut syndrome, review of the literature and a case report Abu Saleh, Tareq Stephen, Lawrence Head Face Med Case Report BACKGROUND: Lennox-Gastaut syndrome (LGS) is a severe form of childhood epilepsy that is defined by generalized multiple type seizures, slowness of intellectual growth, and a specific EEG disturbance. Children affected might previously have infantile spasms or underlying brain disorder but etiology can be idiopathic. In South Africa, the incidence of secondary epilepsy is higher than what is found in developed countries resulting in higher incidence of the disease. LGS seizures are often treatment resistant and the long term prognosis is poor. REPORT: A twenty six year old female, presented with anterior open bite, macroglossia, supragingival as well as subgingival calculus. The gingiva was red, swollen and friable and there was generalized bleeding and localized suppuration. The patient had gingival recession. After periodontal therapy a remarkable improvement in oral health status was noted. CONCLUSION: The clinical findings in LGS included facial deformities, periodontitis and gingival swellings. Interdisciplinary treatment of these patients is fundamental and oral attention is of outstanding importance. Non-surgical periodontal therapy was effective in controlling periodontal disease in the reported case, but prevention of periodontal and dental diseases is preferable for this high-risk group of patients. BioMed Central 2008-06-09 /pmc/articles/PMC2483705/ /pubmed/18541034 http://dx.doi.org/10.1186/1746-160X-4-9 Text en Copyright © 2008 Saleh and Stephen; licensee BioMed Central Ltd. http://creativecommons.org/licenses/by/2.0 This is an Open Access article distributed under the terms of the Creative Commons Attribution License ( (http://creativecommons.org/licenses/by/2.0) ), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Abu Saleh, Tareq
Stephen, Lawrence
Lennox gastaut syndrome, review of the literature and a case report
title Lennox gastaut syndrome, review of the literature and a case report
title_full Lennox gastaut syndrome, review of the literature and a case report
title_fullStr Lennox gastaut syndrome, review of the literature and a case report
title_full_unstemmed Lennox gastaut syndrome, review of the literature and a case report
title_short Lennox gastaut syndrome, review of the literature and a case report
title_sort lennox gastaut syndrome, review of the literature and a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2483705/
https://www.ncbi.nlm.nih.gov/pubmed/18541034
http://dx.doi.org/10.1186/1746-160X-4-9
work_keys_str_mv AT abusalehtareq lennoxgastautsyndromereviewoftheliteratureandacasereport
AT stephenlawrence lennoxgastautsyndromereviewoftheliteratureandacasereport