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'Rapunzel syndrome' trichobezoar in a 7-year-old girl: a case report

BACKGROUND: Rapunzel syndrome is a rare type of trichobezoar with an extension of the hair into the small bowel. Clinical presentation is deceptive and vague ranging from abdominal mass to gastrointestinal symptoms. CASE PRESENTATION: We present a 7 years old girl with Rapunzel syndrome, where the t...

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Detalles Bibliográficos
Autores principales: Al Wadan, Ali H, Al Kaff, Hamed, Al Senabani, Jamila, Al Saadi, Azan S
Formato: Texto
Lenguaje:English
Publicado: BioMed Central 2008
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2567304/
https://www.ncbi.nlm.nih.gov/pubmed/18831761
http://dx.doi.org/10.1186/1757-1626-1-205
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author Al Wadan, Ali H
Al Kaff, Hamed
Al Senabani, Jamila
Al Saadi, Azan S
author_facet Al Wadan, Ali H
Al Kaff, Hamed
Al Senabani, Jamila
Al Saadi, Azan S
author_sort Al Wadan, Ali H
collection PubMed
description BACKGROUND: Rapunzel syndrome is a rare type of trichobezoar with an extension of the hair into the small bowel. Clinical presentation is deceptive and vague ranging from abdominal mass to gastrointestinal symptoms. CASE PRESENTATION: We present a 7 years old girl with Rapunzel syndrome, where the trichobezoar was not suspected at all especially with negative history of trichophagia. In majority of the cases the diagnosis was made very late in the history of the disease, at a stage where surgery is the only cure for this syndrome. CONCLUSION: In the paediatric age group with a long history of gastrointestinal symptom, endoscopy is a diagnostic as well as a therapeutic modality and may reduce surgery in trichobezoars.
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spelling pubmed-25673042008-10-15 'Rapunzel syndrome' trichobezoar in a 7-year-old girl: a case report Al Wadan, Ali H Al Kaff, Hamed Al Senabani, Jamila Al Saadi, Azan S Cases J Case Report BACKGROUND: Rapunzel syndrome is a rare type of trichobezoar with an extension of the hair into the small bowel. Clinical presentation is deceptive and vague ranging from abdominal mass to gastrointestinal symptoms. CASE PRESENTATION: We present a 7 years old girl with Rapunzel syndrome, where the trichobezoar was not suspected at all especially with negative history of trichophagia. In majority of the cases the diagnosis was made very late in the history of the disease, at a stage where surgery is the only cure for this syndrome. CONCLUSION: In the paediatric age group with a long history of gastrointestinal symptom, endoscopy is a diagnostic as well as a therapeutic modality and may reduce surgery in trichobezoars. BioMed Central 2008-10-02 /pmc/articles/PMC2567304/ /pubmed/18831761 http://dx.doi.org/10.1186/1757-1626-1-205 Text en Copyright © 2008 Al Wadan et al; licensee BioMed Central Ltd. http://creativecommons.org/licenses/by/2.0 This is an Open Access article distributed under the terms of the Creative Commons Attribution License ( (http://creativecommons.org/licenses/by/2.0) ), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Al Wadan, Ali H
Al Kaff, Hamed
Al Senabani, Jamila
Al Saadi, Azan S
'Rapunzel syndrome' trichobezoar in a 7-year-old girl: a case report
title 'Rapunzel syndrome' trichobezoar in a 7-year-old girl: a case report
title_full 'Rapunzel syndrome' trichobezoar in a 7-year-old girl: a case report
title_fullStr 'Rapunzel syndrome' trichobezoar in a 7-year-old girl: a case report
title_full_unstemmed 'Rapunzel syndrome' trichobezoar in a 7-year-old girl: a case report
title_short 'Rapunzel syndrome' trichobezoar in a 7-year-old girl: a case report
title_sort 'rapunzel syndrome' trichobezoar in a 7-year-old girl: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2567304/
https://www.ncbi.nlm.nih.gov/pubmed/18831761
http://dx.doi.org/10.1186/1757-1626-1-205
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