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Gorham's disease involving the left parietal bone: a case report

INTRODUCTION: Gorham's disease is a rare bone disease, is characterized by the proliferation of thin-walled vascular channels associated with regional osteolysis. There have been fewer than 150 cases reported in the literature. Shoulder and pelvic region is common site. Skull is the least commo...

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Detalles Bibliográficos
Autores principales: Parihar, Vijay, Yadav, Yad Ram, Sharma, Dhananjaya
Formato: Texto
Lenguaje:English
Publicado: BioMed Central 2008
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2580766/
https://www.ncbi.nlm.nih.gov/pubmed/18940015
http://dx.doi.org/10.1186/1757-1626-1-258
Descripción
Sumario:INTRODUCTION: Gorham's disease is a rare bone disease, is characterized by the proliferation of thin-walled vascular channels associated with regional osteolysis. There have been fewer than 150 cases reported in the literature. Shoulder and pelvic region is common site. Skull is the least common site of involvement. CASE PRESENTATION: We describe a case of a 35-year-old female of Indian origin presented with this rare condition involving her left parietal bone. She was treated successfully with excision of diseased bone and cranioplasty. CONCLUSION: This is the first reported case in India. We provide a review of the clinical, radiological and pathological diagnosis of this rare condition and describe treatment options.