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Bile composition in Alagille Syndrome and PFIC patients having Partial External Biliary Diversion

BACKGROUND: Partial External Biliary Diversion (PEBD) is a surgical intervention to treat children with Progressive Familial Intrahepatic Cholestasis (PFIC) and Alagille syndrome (AGS). PEBD can reduce disease progression, and examining the alterations in biliary lipid composition may be a prognosti...

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Detalles Bibliográficos
Autores principales:	Emerick, Karan M, Elias, Marc S, Melin-Aldana, Hector, Strautnieks, Sandra, Thompson, Richard J, Bull, Laura N, Knisely, AS, Whitington, Peter F, Green, Richard M
Formato:	Texto
Lenguaje:	English
Publicado:	BioMed Central 2008
Materias:	Research Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2585081/ https://www.ncbi.nlm.nih.gov/pubmed/18937870 http://dx.doi.org/10.1186/1471-230X-8-47

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