Cargando…

Gene therapy for inborn errors of liver metabolism: progress towards clinical applications

The treatment for inborn errors of liver metabolism is based on dietary, drug, and cell therapies (orthotopic liver transplantation). However, significant morbidity and mortality still remain, and alternative strategies are needed. Gene replacement therapy has the potential of providing a definitive...

Descripción completa

Detalles Bibliográficos
Autor principal: Brunetti-Pierri, Nicola
Formato: Texto
Lenguaje:English
Publicado: BioMed Central 2008
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2603013/
https://www.ncbi.nlm.nih.gov/pubmed/19490653
http://dx.doi.org/10.1186/1824-7288-34-2
_version_ 1782162550722396160
author Brunetti-Pierri, Nicola
author_facet Brunetti-Pierri, Nicola
author_sort Brunetti-Pierri, Nicola
collection PubMed
description The treatment for inborn errors of liver metabolism is based on dietary, drug, and cell therapies (orthotopic liver transplantation). However, significant morbidity and mortality still remain, and alternative strategies are needed. Gene replacement therapy has the potential of providing a definitive cure for patients with these diseases. Significant progress has been made in the pre-clinical arena and achievement of efficacy in different animal models has been reported using multiple gene transfer technologies. This article summarizes the gene transfer strategies being investigated, the pre-clinical data, and the available early clinical results for inborn errors of liver metabolism.
format Text
id pubmed-2603013
institution National Center for Biotechnology Information
language English
publishDate 2008
publisher BioMed Central
record_format MEDLINE/PubMed
spelling pubmed-26030132009-05-30 Gene therapy for inborn errors of liver metabolism: progress towards clinical applications Brunetti-Pierri, Nicola Ital J Pediatr Review The treatment for inborn errors of liver metabolism is based on dietary, drug, and cell therapies (orthotopic liver transplantation). However, significant morbidity and mortality still remain, and alternative strategies are needed. Gene replacement therapy has the potential of providing a definitive cure for patients with these diseases. Significant progress has been made in the pre-clinical arena and achievement of efficacy in different animal models has been reported using multiple gene transfer technologies. This article summarizes the gene transfer strategies being investigated, the pre-clinical data, and the available early clinical results for inborn errors of liver metabolism. BioMed Central 2008-11-18 /pmc/articles/PMC2603013/ /pubmed/19490653 http://dx.doi.org/10.1186/1824-7288-34-2 Text en Copyright © 2008 Brunetti-Pierri; licensee BioMed Central Ltd. http://creativecommons.org/licenses/by/2.0 This is an Open Access article distributed under the terms of the Creative Commons Attribution License ( (http://creativecommons.org/licenses/by/2.0) ), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Review
Brunetti-Pierri, Nicola
Gene therapy for inborn errors of liver metabolism: progress towards clinical applications
title Gene therapy for inborn errors of liver metabolism: progress towards clinical applications
title_full Gene therapy for inborn errors of liver metabolism: progress towards clinical applications
title_fullStr Gene therapy for inborn errors of liver metabolism: progress towards clinical applications
title_full_unstemmed Gene therapy for inborn errors of liver metabolism: progress towards clinical applications
title_short Gene therapy for inborn errors of liver metabolism: progress towards clinical applications
title_sort gene therapy for inborn errors of liver metabolism: progress towards clinical applications
topic Review
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2603013/
https://www.ncbi.nlm.nih.gov/pubmed/19490653
http://dx.doi.org/10.1186/1824-7288-34-2
work_keys_str_mv AT brunettipierrinicola genetherapyforinbornerrorsoflivermetabolismprogresstowardsclinicalapplications