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Diagnosis of the Double Aortic Arch and Its Differentiation from the Conotruncal Malformations

PURPOSE: The clinical and radiological characteristics of the double aortic arch (DAA) and its differentiation from conotruncal malformations (CTM) were reported in order to familiarize pediatric practitioners with these congenital heart diseases. MATERIALS AND METHODS: From July 1994 to December 20...

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Autor principal: Lee, Meng-Luen
Formato: Texto
Lenguaje:English
Publicado: Yonsei University College of Medicine 2007
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2628149/
https://www.ncbi.nlm.nih.gov/pubmed/17963340
http://dx.doi.org/10.3349/ymj.2007.48.5.818
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author Lee, Meng-Luen
author_facet Lee, Meng-Luen
author_sort Lee, Meng-Luen
collection PubMed
description PURPOSE: The clinical and radiological characteristics of the double aortic arch (DAA) and its differentiation from conotruncal malformations (CTM) were reported in order to familiarize pediatric practitioners with these congenital heart diseases. MATERIALS AND METHODS: From July 1994 to December 2006, a total of 6 patients (4 male and 2 female, aged 16 days to 6.5 years) with DAA were enrolled in this retrospective study. The study modalities included chart recordings, plain chest radiographs, barium esophagograms, echocardiograms, cardiac catheterization, cardiac angiograms, surgery, magnetic resonance imaging, and chromosome analysis. Patients with incomplete vascular rings or with right aortic arches and left ligamentum were excluded. In addition, the clinical and radiological profiles of 38 patients with CTM, including dextro-transposition of the great arteries (d-TGA) (n = 28), hemitruncus arteriosus (HTA) (n = 3), type I truncus arteriosus (TA) (n = 4), and the aortopulmonary window (APW) (n = 3), were comparatively reviewed. RESULTS: All 6 patients with DAA presented with postprandial choking and respiratory distress that prompted their initial visit to the hospital. One of the 6 patients presented with congestive heart failure, and none with cyanosis. Esophagograms showed indentations in 5 patients with DAA. All patients with d-TGA presented with cyanosis and heart failure, while patients with HTA, type I TA, and APW manifested overt heart failure. Suprasternal and subcostal approaches of the echocardiography may offer diagnositic windows for DAA. As for CTM, parasternal and subcostal approaches could always determine the causality. Cardiac catheterization with angiography comprehensively delineated the pathology. CONCLUSION: In case of postprandial choking and respiratory distress in neonates and infants, barium esophagograms can indicate the presence of DAA. Diagnosis of DAA and its differentiation from the CTM can be achieved by echocardiography, angiography, or magnetic resonance imaging.
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spelling pubmed-26281492009-02-02 Diagnosis of the Double Aortic Arch and Its Differentiation from the Conotruncal Malformations Lee, Meng-Luen Yonsei Med J Original Article PURPOSE: The clinical and radiological characteristics of the double aortic arch (DAA) and its differentiation from conotruncal malformations (CTM) were reported in order to familiarize pediatric practitioners with these congenital heart diseases. MATERIALS AND METHODS: From July 1994 to December 2006, a total of 6 patients (4 male and 2 female, aged 16 days to 6.5 years) with DAA were enrolled in this retrospective study. The study modalities included chart recordings, plain chest radiographs, barium esophagograms, echocardiograms, cardiac catheterization, cardiac angiograms, surgery, magnetic resonance imaging, and chromosome analysis. Patients with incomplete vascular rings or with right aortic arches and left ligamentum were excluded. In addition, the clinical and radiological profiles of 38 patients with CTM, including dextro-transposition of the great arteries (d-TGA) (n = 28), hemitruncus arteriosus (HTA) (n = 3), type I truncus arteriosus (TA) (n = 4), and the aortopulmonary window (APW) (n = 3), were comparatively reviewed. RESULTS: All 6 patients with DAA presented with postprandial choking and respiratory distress that prompted their initial visit to the hospital. One of the 6 patients presented with congestive heart failure, and none with cyanosis. Esophagograms showed indentations in 5 patients with DAA. All patients with d-TGA presented with cyanosis and heart failure, while patients with HTA, type I TA, and APW manifested overt heart failure. Suprasternal and subcostal approaches of the echocardiography may offer diagnositic windows for DAA. As for CTM, parasternal and subcostal approaches could always determine the causality. Cardiac catheterization with angiography comprehensively delineated the pathology. CONCLUSION: In case of postprandial choking and respiratory distress in neonates and infants, barium esophagograms can indicate the presence of DAA. Diagnosis of DAA and its differentiation from the CTM can be achieved by echocardiography, angiography, or magnetic resonance imaging. Yonsei University College of Medicine 2007-10-31 2007-10-31 /pmc/articles/PMC2628149/ /pubmed/17963340 http://dx.doi.org/10.3349/ymj.2007.48.5.818 Text en Copyright © 2007 The Yonsei University College of Medicine http://creativecommons.org/licenses/by-nc/3.0 This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0) which permits unrestricted noncommercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Original Article
Lee, Meng-Luen
Diagnosis of the Double Aortic Arch and Its Differentiation from the Conotruncal Malformations
title Diagnosis of the Double Aortic Arch and Its Differentiation from the Conotruncal Malformations
title_full Diagnosis of the Double Aortic Arch and Its Differentiation from the Conotruncal Malformations
title_fullStr Diagnosis of the Double Aortic Arch and Its Differentiation from the Conotruncal Malformations
title_full_unstemmed Diagnosis of the Double Aortic Arch and Its Differentiation from the Conotruncal Malformations
title_short Diagnosis of the Double Aortic Arch and Its Differentiation from the Conotruncal Malformations
title_sort diagnosis of the double aortic arch and its differentiation from the conotruncal malformations
topic Original Article
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2628149/
https://www.ncbi.nlm.nih.gov/pubmed/17963340
http://dx.doi.org/10.3349/ymj.2007.48.5.818
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