Recurrent retroperitoneal hemorrhage in a patient with tuberous sclerosis complex: a case report

BACKGROUND: Tuberous sclerosis complex (TSC) is an autosomal dominant disorder. It is characterized by seizures, mental retardation and hamartomatous lesions, including facial angiofibroma, subependymal giant cell astrocytoma, cardiac rhabdomyoma and renal angiomyolipoma (AML). AMLs can bleed severe...

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Detalles Bibliográficos
Autores principales: Chiarugi, Massimo, Martino, Maria Carola, Pucciarelli, Marsia, Decanini, Luigi, Vignali, Claudio
Formato: Texto
Lenguaje:English
Publicado: BioMed Central 2008
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2636789/
https://www.ncbi.nlm.nih.gov/pubmed/19115994
http://dx.doi.org/10.1186/1757-1626-1-424
Descripción
Sumario:BACKGROUND: Tuberous sclerosis complex (TSC) is an autosomal dominant disorder. It is characterized by seizures, mental retardation and hamartomatous lesions, including facial angiofibroma, subependymal giant cell astrocytoma, cardiac rhabdomyoma and renal angiomyolipoma (AML). AMLs can bleed severely in the retroperitoneal space. CASE PRESENTATION: Herein, we present the case of a TSC patient presenting with recurrent severe episodes of retroperitoneal hemorrhage from AMLs successfully managed by angio-embolization. CONCLUSION: Transarterial embolization is effective in preventing and controlling hemorrhage in patients with AMLs of the kidney

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