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Deciphering von Hippel-Lindau (VHL/Vhl)-Associated Pancreatic Manifestations by Inactivating Vhl in Specific Pancreatic Cell Populations

The von Hippel-Lindau (VHL) syndrome is a pleomorphic familial disease characterized by the development of highly vascularized tumors, such as hemangioblastomas of the central nervous system, pheochromocytomas, renal cell carcinomas, cysts and neuroendocrine tumors of the pancreas. Up to 75% of VHL...

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Detalles Bibliográficos
Autores principales:	Shen, H.-C. Jennifer, Adem, Asha, Ylaya, Kris, Wilson, Arianne, He, Mei, Lorang, Dominique, Hewitt, Stephen M., Pechhold, Klaus, Harlan, David M., Lubensky, Irina A., Schmidt, Laura S., Linehan, W. Marston, Libutti, Steven K.
Formato:	Texto
Lenguaje:	English
Publicado:	Public Library of Science 2009
Materias:	Research Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2660574/ https://www.ncbi.nlm.nih.gov/pubmed/19340311 http://dx.doi.org/10.1371/journal.pone.0004897

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