Juvenile Paget's Disease with Paranasal Sinus Aplasia

Juvenile Paget's disease (JPD) is a rare skeletal disorder that's characterized by bone demineralization and elevated levels of serum alkaline phosphatase. JPD involves the paranasal sinuses in extremely rare cases. We report here on a 25-month-old Asian male who was diagnosed of JPD assoc...

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Detalles Bibliográficos
Autores principales: Bae, Ki Beom, Kwon, Jae Hwan, Kim, Young Ho, Jung, Tae Young, Cho, Joong Hwan
Formato: Texto
Lenguaje:English
Publicado: Korean Society of Otorhinolaryngology-Head and Neck Surgery 2008
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2671770/
https://www.ncbi.nlm.nih.gov/pubmed/19434273
http://dx.doi.org/10.3342/ceo.2008.1.4.224
Descripción
Sumario:Juvenile Paget's disease (JPD) is a rare skeletal disorder that's characterized by bone demineralization and elevated levels of serum alkaline phosphatase. JPD involves the paranasal sinuses in extremely rare cases. We report here on a 25-month-old Asian male who was diagnosed of JPD associated with aplasia of the paranasal sinuses, but not the ethmoid sinuses. The patient was successfully treated by surgery and we undertook no medical intervention. This appears to be the first reported case of JPD associated with bilateral paranasal sinus aplasia.

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