Juvenile Paget's Disease with Paranasal Sinus Aplasia

Juvenile Paget's disease (JPD) is a rare skeletal disorder that's characterized by bone demineralization and elevated levels of serum alkaline phosphatase. JPD involves the paranasal sinuses in extremely rare cases. We report here on a 25-month-old Asian male who was diagnosed of JPD assoc...

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Autores principales: Bae, Ki Beom, Kwon, Jae Hwan, Kim, Young Ho, Jung, Tae Young, Cho, Joong Hwan
Formato: Texto
Lenguaje:English
Publicado: Korean Society of Otorhinolaryngology-Head and Neck Surgery 2008
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2671770/
https://www.ncbi.nlm.nih.gov/pubmed/19434273
http://dx.doi.org/10.3342/ceo.2008.1.4.224
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author Bae, Ki Beom
Kwon, Jae Hwan
Kim, Young Ho
Jung, Tae Young
Cho, Joong Hwan
author_facet Bae, Ki Beom
Kwon, Jae Hwan
Kim, Young Ho
Jung, Tae Young
Cho, Joong Hwan
author_sort Bae, Ki Beom
collection PubMed
description Juvenile Paget's disease (JPD) is a rare skeletal disorder that's characterized by bone demineralization and elevated levels of serum alkaline phosphatase. JPD involves the paranasal sinuses in extremely rare cases. We report here on a 25-month-old Asian male who was diagnosed of JPD associated with aplasia of the paranasal sinuses, but not the ethmoid sinuses. The patient was successfully treated by surgery and we undertook no medical intervention. This appears to be the first reported case of JPD associated with bilateral paranasal sinus aplasia.
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spelling pubmed-26717702009-05-11 Juvenile Paget's Disease with Paranasal Sinus Aplasia Bae, Ki Beom Kwon, Jae Hwan Kim, Young Ho Jung, Tae Young Cho, Joong Hwan Clin Exp Otorhinolaryngol Case Report Juvenile Paget's disease (JPD) is a rare skeletal disorder that's characterized by bone demineralization and elevated levels of serum alkaline phosphatase. JPD involves the paranasal sinuses in extremely rare cases. We report here on a 25-month-old Asian male who was diagnosed of JPD associated with aplasia of the paranasal sinuses, but not the ethmoid sinuses. The patient was successfully treated by surgery and we undertook no medical intervention. This appears to be the first reported case of JPD associated with bilateral paranasal sinus aplasia. Korean Society of Otorhinolaryngology-Head and Neck Surgery 2008-12 2008-12-26 /pmc/articles/PMC2671770/ /pubmed/19434273 http://dx.doi.org/10.3342/ceo.2008.1.4.224 Text en Copyright © 2008 Korean Society of Otorhinolaryngology-Head and Neck Surgery http://creativecommons.org/licenses/by-nc/3.0 This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Bae, Ki Beom
Kwon, Jae Hwan
Kim, Young Ho
Jung, Tae Young
Cho, Joong Hwan
Juvenile Paget's Disease with Paranasal Sinus Aplasia
title Juvenile Paget's Disease with Paranasal Sinus Aplasia
title_full Juvenile Paget's Disease with Paranasal Sinus Aplasia
title_fullStr Juvenile Paget's Disease with Paranasal Sinus Aplasia
title_full_unstemmed Juvenile Paget's Disease with Paranasal Sinus Aplasia
title_short Juvenile Paget's Disease with Paranasal Sinus Aplasia
title_sort juvenile paget's disease with paranasal sinus aplasia
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2671770/
https://www.ncbi.nlm.nih.gov/pubmed/19434273
http://dx.doi.org/10.3342/ceo.2008.1.4.224
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