Para aortic ganglioneuroma presenting as Cushing's syndrome

We present a case of an eight-year-old female presenting with four months history of progressive weight gain, short stature, obesity, mild acanthosis, moon facies and buffalo hump. Biochemically, low-dose and high-dose Dexamethasone tests were not suppressible, ACTH was raised and 24h urinary metane...

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Detalles Bibliográficos
Autores principales: Reddy S., Jaya Ram, Purushottam, G., Pandurangarao, K., Ravi Chander, P. T.
Formato: Texto
Lenguaje:English
Publicado: Medknow Publications 2007
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2721583/
https://www.ncbi.nlm.nih.gov/pubmed/19718307
http://dx.doi.org/10.4103/0970-1591.36725
Descripción
Sumario:We present a case of an eight-year-old female presenting with four months history of progressive weight gain, short stature, obesity, mild acanthosis, moon facies and buffalo hump. Biochemically, low-dose and high-dose Dexamethasone tests were not suppressible, ACTH was raised and 24h urinary metanephrines were normal. The CECT scan showed a 3cm paraganglioma. Tumor was excised via 11(th) rib transcostal approach and the mass was found arising from the sympathetic chain. Histopathology was suggestive of ganglioneuroma positive for ACTH immunostaining.

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