Para aortic ganglioneuroma presenting as Cushing's syndrome

We present a case of an eight-year-old female presenting with four months history of progressive weight gain, short stature, obesity, mild acanthosis, moon facies and buffalo hump. Biochemically, low-dose and high-dose Dexamethasone tests were not suppressible, ACTH was raised and 24h urinary metane...

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Detalles Bibliográficos
Autores principales: Reddy S., Jaya Ram, Purushottam, G., Pandurangarao, K., Ravi Chander, P. T.
Formato: Texto
Lenguaje:English
Publicado: Medknow Publications 2007
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2721583/
https://www.ncbi.nlm.nih.gov/pubmed/19718307
http://dx.doi.org/10.4103/0970-1591.36725
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author Reddy S., Jaya Ram
Purushottam, G.
Pandurangarao, K.
Ravi Chander, P. T.
author_facet Reddy S., Jaya Ram
Purushottam, G.
Pandurangarao, K.
Ravi Chander, P. T.
author_sort Reddy S., Jaya Ram
collection PubMed
description We present a case of an eight-year-old female presenting with four months history of progressive weight gain, short stature, obesity, mild acanthosis, moon facies and buffalo hump. Biochemically, low-dose and high-dose Dexamethasone tests were not suppressible, ACTH was raised and 24h urinary metanephrines were normal. The CECT scan showed a 3cm paraganglioma. Tumor was excised via 11(th) rib transcostal approach and the mass was found arising from the sympathetic chain. Histopathology was suggestive of ganglioneuroma positive for ACTH immunostaining.
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spelling pubmed-27215832009-08-29 Para aortic ganglioneuroma presenting as Cushing's syndrome Reddy S., Jaya Ram Purushottam, G. Pandurangarao, K. Ravi Chander, P. T. Indian J Urol Case Report We present a case of an eight-year-old female presenting with four months history of progressive weight gain, short stature, obesity, mild acanthosis, moon facies and buffalo hump. Biochemically, low-dose and high-dose Dexamethasone tests were not suppressible, ACTH was raised and 24h urinary metanephrines were normal. The CECT scan showed a 3cm paraganglioma. Tumor was excised via 11(th) rib transcostal approach and the mass was found arising from the sympathetic chain. Histopathology was suggestive of ganglioneuroma positive for ACTH immunostaining. Medknow Publications 2007 /pmc/articles/PMC2721583/ /pubmed/19718307 http://dx.doi.org/10.4103/0970-1591.36725 Text en © Indian Journal of Urology http://creativecommons.org/licenses/by/2.0/ This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Reddy S., Jaya Ram
Purushottam, G.
Pandurangarao, K.
Ravi Chander, P. T.
Para aortic ganglioneuroma presenting as Cushing's syndrome
title Para aortic ganglioneuroma presenting as Cushing's syndrome
title_full Para aortic ganglioneuroma presenting as Cushing's syndrome
title_fullStr Para aortic ganglioneuroma presenting as Cushing's syndrome
title_full_unstemmed Para aortic ganglioneuroma presenting as Cushing's syndrome
title_short Para aortic ganglioneuroma presenting as Cushing's syndrome
title_sort para aortic ganglioneuroma presenting as cushing's syndrome
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2721583/
https://www.ncbi.nlm.nih.gov/pubmed/19718307
http://dx.doi.org/10.4103/0970-1591.36725
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AT purushottamg paraaorticganglioneuromapresentingascushingssyndrome
AT pandurangaraok paraaorticganglioneuromapresentingascushingssyndrome
AT ravichanderpt paraaorticganglioneuromapresentingascushingssyndrome

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