Nummular keratopathy in a patient with Hyper-IgD Syndrome

PURPOSE: To report a case of recurrent nummular keratitis in a pediatric patient with Hyperimmunoglobulinemia D syndrome. METHODS: A retrospective chart review. RESULTS: A 14-year-old boy with Hyperimmunoglobulinemia D syndrome (HIDS) presented with photophobia and ocular irritation concomitant with...

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Detalles Bibliográficos
Autores principales: Kraus, Courtney L, Culican, Susan M
Formato: Texto
Lenguaje:English
Publicado: BioMed Central 2009
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2731058/
https://www.ncbi.nlm.nih.gov/pubmed/19656398
http://dx.doi.org/10.1186/1546-0096-7-14
Descripción
Sumario:PURPOSE: To report a case of recurrent nummular keratitis in a pediatric patient with Hyperimmunoglobulinemia D syndrome. METHODS: A retrospective chart review. RESULTS: A 14-year-old boy with Hyperimmunoglobulinemia D syndrome (HIDS) presented with photophobia and ocular irritation concomitant with disease exacerbation. He was found on exam to have significant nummular keratitis, which responded to a short course of topical steroids. Despite acute response to local immunosuppression, the patient had several recurrent attacks and eventually developed a large corneal scar and decreased vision. After initiation of infliximab therapy his ocular sequelae improved dramatically and his vision returned to 20/20. CONCLUSION: One possible form of end-organ damage associated with HIDS is vision threatening nummular keratopathy.

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