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Primitive neuroectodermal tumor of the kidney in an adult: a case report

INTRODUCTION: Primitive neuroectodermal tumors (PNETs) occur predominantly in childhood preferentially in the soft tissues of the lower extremity and the paraspinal region. We present here a rare case of a PNET of the kidney in an adult. CASE PRESENTATION: A tumor adjacent to the right kidney was de...

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Autores principales: Businger, Adrian, Zettl, Andreas, Sonnet, Stefan, Ruszat, Robin, von Flüe, Markus
Formato: Texto
Lenguaje:English
Publicado: Cases Network Ltd 2009
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2740287/
https://www.ncbi.nlm.nih.gov/pubmed/19829861
http://dx.doi.org/10.4076/1757-1626-2-6791
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author Businger, Adrian
Zettl, Andreas
Sonnet, Stefan
Ruszat, Robin
von Flüe, Markus
author_facet Businger, Adrian
Zettl, Andreas
Sonnet, Stefan
Ruszat, Robin
von Flüe, Markus
author_sort Businger, Adrian
collection PubMed
description INTRODUCTION: Primitive neuroectodermal tumors (PNETs) occur predominantly in childhood preferentially in the soft tissues of the lower extremity and the paraspinal region. We present here a rare case of a PNET of the kidney in an adult. CASE PRESENTATION: A tumor adjacent to the right kidney was detected by ultrasound coincidentally at a routine check-up in a 46-year-old woman with irritable bowel syndrome in her medical history. The patient had no clinical signs. Contrast-enhanced computerized tomography scan of the abdomen demonstrated a highly vascularized renal tumor. A retroperitonealectomy with en-bloc resection of the kidney was performed, and histopathological work-up showed a primitive neuroectodermal tumor of the kidney with the characteristic translocation t(11;22)(q24;q12). CONCLUSION: This tumor entity must be accurately distinguished from other renal neoplasms because of the prognostic and therapeutic impact.
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spelling pubmed-27402872009-10-14 Primitive neuroectodermal tumor of the kidney in an adult: a case report Businger, Adrian Zettl, Andreas Sonnet, Stefan Ruszat, Robin von Flüe, Markus Cases J Case report INTRODUCTION: Primitive neuroectodermal tumors (PNETs) occur predominantly in childhood preferentially in the soft tissues of the lower extremity and the paraspinal region. We present here a rare case of a PNET of the kidney in an adult. CASE PRESENTATION: A tumor adjacent to the right kidney was detected by ultrasound coincidentally at a routine check-up in a 46-year-old woman with irritable bowel syndrome in her medical history. The patient had no clinical signs. Contrast-enhanced computerized tomography scan of the abdomen demonstrated a highly vascularized renal tumor. A retroperitonealectomy with en-bloc resection of the kidney was performed, and histopathological work-up showed a primitive neuroectodermal tumor of the kidney with the characteristic translocation t(11;22)(q24;q12). CONCLUSION: This tumor entity must be accurately distinguished from other renal neoplasms because of the prognostic and therapeutic impact. Cases Network Ltd 2009-06-05 /pmc/articles/PMC2740287/ /pubmed/19829861 http://dx.doi.org/10.4076/1757-1626-2-6791 Text en © 2009 Businger et al.; licensee Cases Network Ltd. http://creativecommons.org/licenses/by/3.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/3.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case report
Businger, Adrian
Zettl, Andreas
Sonnet, Stefan
Ruszat, Robin
von Flüe, Markus
Primitive neuroectodermal tumor of the kidney in an adult: a case report
title Primitive neuroectodermal tumor of the kidney in an adult: a case report
title_full Primitive neuroectodermal tumor of the kidney in an adult: a case report
title_fullStr Primitive neuroectodermal tumor of the kidney in an adult: a case report
title_full_unstemmed Primitive neuroectodermal tumor of the kidney in an adult: a case report
title_short Primitive neuroectodermal tumor of the kidney in an adult: a case report
title_sort primitive neuroectodermal tumor of the kidney in an adult: a case report
topic Case report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2740287/
https://www.ncbi.nlm.nih.gov/pubmed/19829861
http://dx.doi.org/10.4076/1757-1626-2-6791
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