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Primitive neuroectodermal tumor of the kidney in an adult: a case report
INTRODUCTION: Primitive neuroectodermal tumors (PNETs) occur predominantly in childhood preferentially in the soft tissues of the lower extremity and the paraspinal region. We present here a rare case of a PNET of the kidney in an adult. CASE PRESENTATION: A tumor adjacent to the right kidney was de...
Autores principales: | , , , , |
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Formato: | Texto |
Lenguaje: | English |
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Cases Network Ltd
2009
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2740287/ https://www.ncbi.nlm.nih.gov/pubmed/19829861 http://dx.doi.org/10.4076/1757-1626-2-6791 |
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author | Businger, Adrian Zettl, Andreas Sonnet, Stefan Ruszat, Robin von Flüe, Markus |
author_facet | Businger, Adrian Zettl, Andreas Sonnet, Stefan Ruszat, Robin von Flüe, Markus |
author_sort | Businger, Adrian |
collection | PubMed |
description | INTRODUCTION: Primitive neuroectodermal tumors (PNETs) occur predominantly in childhood preferentially in the soft tissues of the lower extremity and the paraspinal region. We present here a rare case of a PNET of the kidney in an adult. CASE PRESENTATION: A tumor adjacent to the right kidney was detected by ultrasound coincidentally at a routine check-up in a 46-year-old woman with irritable bowel syndrome in her medical history. The patient had no clinical signs. Contrast-enhanced computerized tomography scan of the abdomen demonstrated a highly vascularized renal tumor. A retroperitonealectomy with en-bloc resection of the kidney was performed, and histopathological work-up showed a primitive neuroectodermal tumor of the kidney with the characteristic translocation t(11;22)(q24;q12). CONCLUSION: This tumor entity must be accurately distinguished from other renal neoplasms because of the prognostic and therapeutic impact. |
format | Text |
id | pubmed-2740287 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2009 |
publisher | Cases Network Ltd |
record_format | MEDLINE/PubMed |
spelling | pubmed-27402872009-10-14 Primitive neuroectodermal tumor of the kidney in an adult: a case report Businger, Adrian Zettl, Andreas Sonnet, Stefan Ruszat, Robin von Flüe, Markus Cases J Case report INTRODUCTION: Primitive neuroectodermal tumors (PNETs) occur predominantly in childhood preferentially in the soft tissues of the lower extremity and the paraspinal region. We present here a rare case of a PNET of the kidney in an adult. CASE PRESENTATION: A tumor adjacent to the right kidney was detected by ultrasound coincidentally at a routine check-up in a 46-year-old woman with irritable bowel syndrome in her medical history. The patient had no clinical signs. Contrast-enhanced computerized tomography scan of the abdomen demonstrated a highly vascularized renal tumor. A retroperitonealectomy with en-bloc resection of the kidney was performed, and histopathological work-up showed a primitive neuroectodermal tumor of the kidney with the characteristic translocation t(11;22)(q24;q12). CONCLUSION: This tumor entity must be accurately distinguished from other renal neoplasms because of the prognostic and therapeutic impact. Cases Network Ltd 2009-06-05 /pmc/articles/PMC2740287/ /pubmed/19829861 http://dx.doi.org/10.4076/1757-1626-2-6791 Text en © 2009 Businger et al.; licensee Cases Network Ltd. http://creativecommons.org/licenses/by/3.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/3.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case report Businger, Adrian Zettl, Andreas Sonnet, Stefan Ruszat, Robin von Flüe, Markus Primitive neuroectodermal tumor of the kidney in an adult: a case report |
title | Primitive neuroectodermal tumor of the kidney in an adult: a case report |
title_full | Primitive neuroectodermal tumor of the kidney in an adult: a case report |
title_fullStr | Primitive neuroectodermal tumor of the kidney in an adult: a case report |
title_full_unstemmed | Primitive neuroectodermal tumor of the kidney in an adult: a case report |
title_short | Primitive neuroectodermal tumor of the kidney in an adult: a case report |
title_sort | primitive neuroectodermal tumor of the kidney in an adult: a case report |
topic | Case report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2740287/ https://www.ncbi.nlm.nih.gov/pubmed/19829861 http://dx.doi.org/10.4076/1757-1626-2-6791 |
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