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Absent pulmonary valve syndrome with tetralogy of Fallot and associated dextrocardia detected at an early gestational age of 26 weeks
Absent pulmonary valve syndrome is a rare congenital anomaly, usually seen in association with a ventricular septal defect. It has been reported to occur in 3–6% of cases of tetralogy of Fallot. Absence of the pulmonary valve results in a dilated main pulmonary artery, which can be seen as a cystic,...
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Formato: | Texto |
Lenguaje: | English |
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Medknow Publications
2008
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Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2747463/ https://www.ncbi.nlm.nih.gov/pubmed/19774197 http://dx.doi.org/10.4103/0971-3026.43841 |
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author | Bharati, Alpa H Naware, Ajita Merchant, Suleman A |
author_facet | Bharati, Alpa H Naware, Ajita Merchant, Suleman A |
author_sort | Bharati, Alpa H |
collection | PubMed |
description | Absent pulmonary valve syndrome is a rare congenital anomaly, usually seen in association with a ventricular septal defect. It has been reported to occur in 3–6% of cases of tetralogy of Fallot. Absence of the pulmonary valve results in a dilated main pulmonary artery, which can be seen as a cystic, pulsatile, paracardiac lesion on antenatal USG. Such a lesion, though rare, can easily be detected. We report a case of this rare anomaly which was present in association with a ventricular septal defect, tetralogy of Fallot, and dextrocardia. The case was detected at 26 weeks of gestation. |
format | Text |
id | pubmed-2747463 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2008 |
publisher | Medknow Publications |
record_format | MEDLINE/PubMed |
spelling | pubmed-27474632009-09-22 Absent pulmonary valve syndrome with tetralogy of Fallot and associated dextrocardia detected at an early gestational age of 26 weeks Bharati, Alpa H Naware, Ajita Merchant, Suleman A Indian J Radiol Imaging Obstetric USG Symposium Absent pulmonary valve syndrome is a rare congenital anomaly, usually seen in association with a ventricular septal defect. It has been reported to occur in 3–6% of cases of tetralogy of Fallot. Absence of the pulmonary valve results in a dilated main pulmonary artery, which can be seen as a cystic, pulsatile, paracardiac lesion on antenatal USG. Such a lesion, though rare, can easily be detected. We report a case of this rare anomaly which was present in association with a ventricular septal defect, tetralogy of Fallot, and dextrocardia. The case was detected at 26 weeks of gestation. Medknow Publications 2008-11 /pmc/articles/PMC2747463/ /pubmed/19774197 http://dx.doi.org/10.4103/0971-3026.43841 Text en © Indian Journal of Radiology and Imaging http://creativecommons.org/licenses/by/2.0/ This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Obstetric USG Symposium Bharati, Alpa H Naware, Ajita Merchant, Suleman A Absent pulmonary valve syndrome with tetralogy of Fallot and associated dextrocardia detected at an early gestational age of 26 weeks |
title | Absent pulmonary valve syndrome with tetralogy of Fallot and associated dextrocardia detected at an early gestational age of 26 weeks |
title_full | Absent pulmonary valve syndrome with tetralogy of Fallot and associated dextrocardia detected at an early gestational age of 26 weeks |
title_fullStr | Absent pulmonary valve syndrome with tetralogy of Fallot and associated dextrocardia detected at an early gestational age of 26 weeks |
title_full_unstemmed | Absent pulmonary valve syndrome with tetralogy of Fallot and associated dextrocardia detected at an early gestational age of 26 weeks |
title_short | Absent pulmonary valve syndrome with tetralogy of Fallot and associated dextrocardia detected at an early gestational age of 26 weeks |
title_sort | absent pulmonary valve syndrome with tetralogy of fallot and associated dextrocardia detected at an early gestational age of 26 weeks |
topic | Obstetric USG Symposium |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2747463/ https://www.ncbi.nlm.nih.gov/pubmed/19774197 http://dx.doi.org/10.4103/0971-3026.43841 |
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