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Absent pulmonary valve syndrome with tetralogy of Fallot and associated dextrocardia detected at an early gestational age of 26 weeks

Absent pulmonary valve syndrome is a rare congenital anomaly, usually seen in association with a ventricular septal defect. It has been reported to occur in 3–6% of cases of tetralogy of Fallot. Absence of the pulmonary valve results in a dilated main pulmonary artery, which can be seen as a cystic,...

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Autores principales: Bharati, Alpa H, Naware, Ajita, Merchant, Suleman A
Formato: Texto
Lenguaje:English
Publicado: Medknow Publications 2008
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2747463/
https://www.ncbi.nlm.nih.gov/pubmed/19774197
http://dx.doi.org/10.4103/0971-3026.43841
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author Bharati, Alpa H
Naware, Ajita
Merchant, Suleman A
author_facet Bharati, Alpa H
Naware, Ajita
Merchant, Suleman A
author_sort Bharati, Alpa H
collection PubMed
description Absent pulmonary valve syndrome is a rare congenital anomaly, usually seen in association with a ventricular septal defect. It has been reported to occur in 3–6% of cases of tetralogy of Fallot. Absence of the pulmonary valve results in a dilated main pulmonary artery, which can be seen as a cystic, pulsatile, paracardiac lesion on antenatal USG. Such a lesion, though rare, can easily be detected. We report a case of this rare anomaly which was present in association with a ventricular septal defect, tetralogy of Fallot, and dextrocardia. The case was detected at 26 weeks of gestation.
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spelling pubmed-27474632009-09-22 Absent pulmonary valve syndrome with tetralogy of Fallot and associated dextrocardia detected at an early gestational age of 26 weeks Bharati, Alpa H Naware, Ajita Merchant, Suleman A Indian J Radiol Imaging Obstetric USG Symposium Absent pulmonary valve syndrome is a rare congenital anomaly, usually seen in association with a ventricular septal defect. It has been reported to occur in 3–6% of cases of tetralogy of Fallot. Absence of the pulmonary valve results in a dilated main pulmonary artery, which can be seen as a cystic, pulsatile, paracardiac lesion on antenatal USG. Such a lesion, though rare, can easily be detected. We report a case of this rare anomaly which was present in association with a ventricular septal defect, tetralogy of Fallot, and dextrocardia. The case was detected at 26 weeks of gestation. Medknow Publications 2008-11 /pmc/articles/PMC2747463/ /pubmed/19774197 http://dx.doi.org/10.4103/0971-3026.43841 Text en © Indian Journal of Radiology and Imaging http://creativecommons.org/licenses/by/2.0/ This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Obstetric USG Symposium
Bharati, Alpa H
Naware, Ajita
Merchant, Suleman A
Absent pulmonary valve syndrome with tetralogy of Fallot and associated dextrocardia detected at an early gestational age of 26 weeks
title Absent pulmonary valve syndrome with tetralogy of Fallot and associated dextrocardia detected at an early gestational age of 26 weeks
title_full Absent pulmonary valve syndrome with tetralogy of Fallot and associated dextrocardia detected at an early gestational age of 26 weeks
title_fullStr Absent pulmonary valve syndrome with tetralogy of Fallot and associated dextrocardia detected at an early gestational age of 26 weeks
title_full_unstemmed Absent pulmonary valve syndrome with tetralogy of Fallot and associated dextrocardia detected at an early gestational age of 26 weeks
title_short Absent pulmonary valve syndrome with tetralogy of Fallot and associated dextrocardia detected at an early gestational age of 26 weeks
title_sort absent pulmonary valve syndrome with tetralogy of fallot and associated dextrocardia detected at an early gestational age of 26 weeks
topic Obstetric USG Symposium
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2747463/
https://www.ncbi.nlm.nih.gov/pubmed/19774197
http://dx.doi.org/10.4103/0971-3026.43841
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