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Molecular correlates of axonal and synaptic pathology in mouse models of Batten disease
Neuronal ceroid lipofuscinoses (NCLs; Batten disease) are collectively the most frequent autosomal-recessive neurodegenerative disease of childhood, but the underlying cellular and molecular mechanisms remain unclear. Several lines of evidence have highlighted the important role that non-somatic com...
Autores principales: | Kielar, Catherine, Wishart, Thomas M., Palmer, Alice, Dihanich, Sybille, Wong, Andrew M., Macauley, Shannon L., Chan, Chun-Hung, Sands, Mark S., Pearce, David A., Cooper, Jonathan D., Gillingwater, Thomas H. |
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Formato: | Texto |
Lenguaje: | English |
Publicado: |
Oxford University Press
2009
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2758138/ https://www.ncbi.nlm.nih.gov/pubmed/19640925 http://dx.doi.org/10.1093/hmg/ddp355 |
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