Papillon-Lefèvre syndrome and squamous cell carcinoma: a case report

Papillon-Lefèvre syndrome is a rare autosomal recessive genodermatosis characterised by palmoplantar hyperkeratosis and severe early-onset periodontitis. The development of malignant cutaneous neoplasms within the hyperkeratotic lesions of the syndrome is very rare. Here, we report on a 67-year-old...

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Autores principales: Al-Benna, Sammy, Hasler, Raphael, Stricker, Ingo, Steinau, Hans-Ulrich, Steinstraesser, Lars
Formato: Texto
Lenguaje:English
Publicado: Cases Network Ltd 2009
Materias:
Case report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2769336/
https://www.ncbi.nlm.nih.gov/pubmed/19918506
http://dx.doi.org/10.4076/1757-1626-2-7067
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author Al-Benna, Sammy
Hasler, Raphael
Stricker, Ingo
Steinau, Hans-Ulrich
Steinstraesser, Lars
author_facet Al-Benna, Sammy
Hasler, Raphael
Stricker, Ingo
Steinau, Hans-Ulrich
Steinstraesser, Lars
author_sort Al-Benna, Sammy
collection PubMed
description Papillon-Lefèvre syndrome is a rare autosomal recessive genodermatosis characterised by palmoplantar hyperkeratosis and severe early-onset periodontitis. The development of malignant cutaneous neoplasms within the hyperkeratotic lesions of the syndrome is very rare. Here, we report on a 67-year-old German Caucasian male with Papillon-Lefèvre syndrome associated with recurrent squamous cell carcinoma. Treatment is symptomatic and not always satisfactory.
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spelling pubmed-27693362009-11-16 Papillon-Lefèvre syndrome and squamous cell carcinoma: a case report Al-Benna, Sammy Hasler, Raphael Stricker, Ingo Steinau, Hans-Ulrich Steinstraesser, Lars Cases J Case report Papillon-Lefèvre syndrome is a rare autosomal recessive genodermatosis characterised by palmoplantar hyperkeratosis and severe early-onset periodontitis. The development of malignant cutaneous neoplasms within the hyperkeratotic lesions of the syndrome is very rare. Here, we report on a 67-year-old German Caucasian male with Papillon-Lefèvre syndrome associated with recurrent squamous cell carcinoma. Treatment is symptomatic and not always satisfactory. Cases Network Ltd 2009-08-28 /pmc/articles/PMC2769336/ /pubmed/19918506 http://dx.doi.org/10.4076/1757-1626-2-7067 Text en © 2009 Al-Benna et al.; licensee Cases Network Ltd. http://creativecommons.org/licenses/by/3.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/3.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case report
Al-Benna, Sammy
Hasler, Raphael
Stricker, Ingo
Steinau, Hans-Ulrich
Steinstraesser, Lars
Papillon-Lefèvre syndrome and squamous cell carcinoma: a case report
title Papillon-Lefèvre syndrome and squamous cell carcinoma: a case report
title_full Papillon-Lefèvre syndrome and squamous cell carcinoma: a case report
title_fullStr Papillon-Lefèvre syndrome and squamous cell carcinoma: a case report
title_full_unstemmed Papillon-Lefèvre syndrome and squamous cell carcinoma: a case report
title_short Papillon-Lefèvre syndrome and squamous cell carcinoma: a case report
title_sort papillon-lefèvre syndrome and squamous cell carcinoma: a case report
topic Case report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2769336/
https://www.ncbi.nlm.nih.gov/pubmed/19918506
http://dx.doi.org/10.4076/1757-1626-2-7067
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AT haslerraphael papillonlefevresyndromeandsquamouscellcarcinomaacasereport
AT strickeringo papillonlefevresyndromeandsquamouscellcarcinomaacasereport
AT steinauhansulrich papillonlefevresyndromeandsquamouscellcarcinomaacasereport
AT steinstraesserlars papillonlefevresyndromeandsquamouscellcarcinomaacasereport

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