Primary mucinous cystadenocarcinoma of renal pelvis: a case report

BACKGROUND: We report a case of primary mucinous cystadenocarcinoma of renal pelvis which radiologically resembled large multicystic mass in 45 years old man. CASE PRESENTATION: The patient referred to our center with loin pain and progressive abdominal distention from 4 years ago. In the previous published literature, four cases of mucinous cystadenocarcinoma of renal origin have been published. Abdominal CT showed complete replacement of left kidney by a large multiloculated cystic mass accompanied with multiple large nephrolithiasis. Nephrectomy was performed and histopathology revealed covering of epithelium of renal pelvis by columnar epithelium and scattered goblet cells and mucous gland. CONCLUSION: Mucinous cystic neoplasms of kidney are rare entity and our case and few similar reported cases showed that this tumor is an unique clinicopathologic renal mass that may be classified by World Health Organization classification in the future