RARE ASSOCIATION OF HYPER IgE SYNDROME WITH CERVICAL RIB AND NATAL TEETH

Hyper IgE syndrome (HIES) is a rare immunodeficiency syndrome characterized by a triad of cutaneous abscesses, mostly caused by Staphylococus aureus; pneumonia; and raised IgE levels. Nonimmunological associations include course facial features, multiple bone fractures, joint hyperextensibility, and...

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Detalles Bibliográficos
Autores principales: Roshan, Anupama S, Janaki, C, Parveen, B, Gomathy, N
Formato: Texto
Lenguaje:English
Publicado: Medknow Publications 2009
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2807717/
https://www.ncbi.nlm.nih.gov/pubmed/20101342
http://dx.doi.org/10.4103/0019-5154.57617
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author Roshan, Anupama S
Janaki, C
Parveen, B
Gomathy, N
author_facet Roshan, Anupama S
Janaki, C
Parveen, B
Gomathy, N
author_sort Roshan, Anupama S
collection PubMed
description Hyper IgE syndrome (HIES) is a rare immunodeficiency syndrome characterized by a triad of cutaneous abscesses, mostly caused by Staphylococus aureus; pneumonia; and raised IgE levels. Nonimmunological associations include course facial features, multiple bone fractures, joint hyperextensibility, and retained primary dentition. Patients require long-term antibiotic therapy. We report here a classical case of HIES with rare associations of natal teeth, bilateral cervical ribs, and conductive deafness. The patient was being treated with monteleukast and dapsone.
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spelling pubmed-28077172010-01-25 RARE ASSOCIATION OF HYPER IgE SYNDROME WITH CERVICAL RIB AND NATAL TEETH Roshan, Anupama S Janaki, C Parveen, B Gomathy, N Indian J Dermatol Case Report Hyper IgE syndrome (HIES) is a rare immunodeficiency syndrome characterized by a triad of cutaneous abscesses, mostly caused by Staphylococus aureus; pneumonia; and raised IgE levels. Nonimmunological associations include course facial features, multiple bone fractures, joint hyperextensibility, and retained primary dentition. Patients require long-term antibiotic therapy. We report here a classical case of HIES with rare associations of natal teeth, bilateral cervical ribs, and conductive deafness. The patient was being treated with monteleukast and dapsone. Medknow Publications 2009 /pmc/articles/PMC2807717/ /pubmed/20101342 http://dx.doi.org/10.4103/0019-5154.57617 Text en © Indian Journal of Dermatology http://creativecommons.org/licenses/by/2.0/ This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Roshan, Anupama S
Janaki, C
Parveen, B
Gomathy, N
RARE ASSOCIATION OF HYPER IgE SYNDROME WITH CERVICAL RIB AND NATAL TEETH
title RARE ASSOCIATION OF HYPER IgE SYNDROME WITH CERVICAL RIB AND NATAL TEETH
title_full RARE ASSOCIATION OF HYPER IgE SYNDROME WITH CERVICAL RIB AND NATAL TEETH
title_fullStr RARE ASSOCIATION OF HYPER IgE SYNDROME WITH CERVICAL RIB AND NATAL TEETH
title_full_unstemmed RARE ASSOCIATION OF HYPER IgE SYNDROME WITH CERVICAL RIB AND NATAL TEETH
title_short RARE ASSOCIATION OF HYPER IgE SYNDROME WITH CERVICAL RIB AND NATAL TEETH
title_sort rare association of hyper ige syndrome with cervical rib and natal teeth
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2807717/
https://www.ncbi.nlm.nih.gov/pubmed/20101342
http://dx.doi.org/10.4103/0019-5154.57617
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AT janakic rareassociationofhyperigesyndromewithcervicalribandnatalteeth
AT parveenb rareassociationofhyperigesyndromewithcervicalribandnatalteeth
AT gomathyn rareassociationofhyperigesyndromewithcervicalribandnatalteeth

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