Assessing a Dysplastic Cerebellar Gangliocytoma (Lhermitte-Duclos Disease) with 7T MR Imaging

Lhermitte-Duclos disease (LDD; dysplastic cerebellar gangliocytoma) is a rare hamartomatous lesion of the cerebellar cortex and this was first described in 1920. LDD is considered to be part of the autosomal-dominant phacomatosis and cancer syndrome Cowden disease (CS). We examined the brain of a 46...

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Autores principales: Moenninghoff, Christoph, Kraff, Oliver, Schlamann, Marc, Ladd, Mark E., Katsarava, Zaza, Gizewski, Elke R.
Formato: Texto
Lenguaje:English
Publicado: The Korean Society of Radiology 2010
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2827790/
https://www.ncbi.nlm.nih.gov/pubmed/20191074
http://dx.doi.org/10.3348/kjr.2010.11.2.244
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author Moenninghoff, Christoph
Kraff, Oliver
Schlamann, Marc
Ladd, Mark E.
Katsarava, Zaza
Gizewski, Elke R.
author_facet Moenninghoff, Christoph
Kraff, Oliver
Schlamann, Marc
Ladd, Mark E.
Katsarava, Zaza
Gizewski, Elke R.
author_sort Moenninghoff, Christoph
collection PubMed
description Lhermitte-Duclos disease (LDD; dysplastic cerebellar gangliocytoma) is a rare hamartomatous lesion of the cerebellar cortex and this was first described in 1920. LDD is considered to be part of the autosomal-dominant phacomatosis and cancer syndrome Cowden disease (CS). We examined the brain of a 46-year-old man, who displayed the manifestations of CS, with 7 Tesla (T) and 1.5T MRI and 1.5T MR spectroscopy ((1)H-MRS). We discuss the possible benefits of employing ultrahigh-field MRI for making the diagnosis of this rare lesion.
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spelling pubmed-28277902010-03-01 Assessing a Dysplastic Cerebellar Gangliocytoma (Lhermitte-Duclos Disease) with 7T MR Imaging Moenninghoff, Christoph Kraff, Oliver Schlamann, Marc Ladd, Mark E. Katsarava, Zaza Gizewski, Elke R. Korean J Radiol Case Report Lhermitte-Duclos disease (LDD; dysplastic cerebellar gangliocytoma) is a rare hamartomatous lesion of the cerebellar cortex and this was first described in 1920. LDD is considered to be part of the autosomal-dominant phacomatosis and cancer syndrome Cowden disease (CS). We examined the brain of a 46-year-old man, who displayed the manifestations of CS, with 7 Tesla (T) and 1.5T MRI and 1.5T MR spectroscopy ((1)H-MRS). We discuss the possible benefits of employing ultrahigh-field MRI for making the diagnosis of this rare lesion. The Korean Society of Radiology 2010 2010-02-22 /pmc/articles/PMC2827790/ /pubmed/20191074 http://dx.doi.org/10.3348/kjr.2010.11.2.244 Text en Copyright © 2010 The Korean Society of Radiology http://creativecommons.org/licenses/by-nc/3.0 This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Moenninghoff, Christoph
Kraff, Oliver
Schlamann, Marc
Ladd, Mark E.
Katsarava, Zaza
Gizewski, Elke R.
Assessing a Dysplastic Cerebellar Gangliocytoma (Lhermitte-Duclos Disease) with 7T MR Imaging
title Assessing a Dysplastic Cerebellar Gangliocytoma (Lhermitte-Duclos Disease) with 7T MR Imaging
title_full Assessing a Dysplastic Cerebellar Gangliocytoma (Lhermitte-Duclos Disease) with 7T MR Imaging
title_fullStr Assessing a Dysplastic Cerebellar Gangliocytoma (Lhermitte-Duclos Disease) with 7T MR Imaging
title_full_unstemmed Assessing a Dysplastic Cerebellar Gangliocytoma (Lhermitte-Duclos Disease) with 7T MR Imaging
title_short Assessing a Dysplastic Cerebellar Gangliocytoma (Lhermitte-Duclos Disease) with 7T MR Imaging
title_sort assessing a dysplastic cerebellar gangliocytoma (lhermitte-duclos disease) with 7t mr imaging
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2827790/
https://www.ncbi.nlm.nih.gov/pubmed/20191074
http://dx.doi.org/10.3348/kjr.2010.11.2.244
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