Anaesthetic considerations of adults with Morquio's syndrome - a case report

BACKGROUND: The anaesthetic management of patients with Morquio syndrome is complicated by a number of factors including odontoid hypoplasia, atlantoaxial instability, thoracic kyphosis, and deposition of mucopolysaccharides in the soft tissue of the oropharnyx. CASE PRESENTATION: Herein we describe...

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Detalles Bibliográficos
Autores principales: McLaughlin, Anne Marie, Farooq, Muhammad, Donnelly, Maria B, Foley, Kieran
Formato: Texto
Lenguaje:English
Publicado: BioMed Central 2010
Materias:
Case report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2841068/
https://www.ncbi.nlm.nih.gov/pubmed/20184780
http://dx.doi.org/10.1186/1471-2253-10-2
Descripción
Sumario:BACKGROUND: The anaesthetic management of patients with Morquio syndrome is complicated by a number of factors including odontoid hypoplasia, atlantoaxial instability, thoracic kyphosis, and deposition of mucopolysaccharides in the soft tissue of the oropharnyx. CASE PRESENTATION: Herein we describe the anaesthetic considerations and management of a 26 year old adult with Morquio syndrome, who presented for an elective hip replacement. CONCLUSION: This report details an awake fiberoptic intubation in an adult with Morquio syndrome. We recommend that this approach be considered in patients with Morquio syndrome undergoing general anaesthesia.

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