Anaesthetic considerations of adults with Morquio's syndrome - a case report

BACKGROUND: The anaesthetic management of patients with Morquio syndrome is complicated by a number of factors including odontoid hypoplasia, atlantoaxial instability, thoracic kyphosis, and deposition of mucopolysaccharides in the soft tissue of the oropharnyx. CASE PRESENTATION: Herein we describe...

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Autores principales: McLaughlin, Anne Marie, Farooq, Muhammad, Donnelly, Maria B, Foley, Kieran
Formato: Texto
Lenguaje:English
Publicado: BioMed Central 2010
Materias:
Case report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2841068/
https://www.ncbi.nlm.nih.gov/pubmed/20184780
http://dx.doi.org/10.1186/1471-2253-10-2
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author McLaughlin, Anne Marie
Farooq, Muhammad
Donnelly, Maria B
Foley, Kieran
author_facet McLaughlin, Anne Marie
Farooq, Muhammad
Donnelly, Maria B
Foley, Kieran
author_sort McLaughlin, Anne Marie
collection PubMed
description BACKGROUND: The anaesthetic management of patients with Morquio syndrome is complicated by a number of factors including odontoid hypoplasia, atlantoaxial instability, thoracic kyphosis, and deposition of mucopolysaccharides in the soft tissue of the oropharnyx. CASE PRESENTATION: Herein we describe the anaesthetic considerations and management of a 26 year old adult with Morquio syndrome, who presented for an elective hip replacement. CONCLUSION: This report details an awake fiberoptic intubation in an adult with Morquio syndrome. We recommend that this approach be considered in patients with Morquio syndrome undergoing general anaesthesia.
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spelling pubmed-28410682010-03-18 Anaesthetic considerations of adults with Morquio's syndrome - a case report McLaughlin, Anne Marie Farooq, Muhammad Donnelly, Maria B Foley, Kieran BMC Anesthesiol Case report BACKGROUND: The anaesthetic management of patients with Morquio syndrome is complicated by a number of factors including odontoid hypoplasia, atlantoaxial instability, thoracic kyphosis, and deposition of mucopolysaccharides in the soft tissue of the oropharnyx. CASE PRESENTATION: Herein we describe the anaesthetic considerations and management of a 26 year old adult with Morquio syndrome, who presented for an elective hip replacement. CONCLUSION: This report details an awake fiberoptic intubation in an adult with Morquio syndrome. We recommend that this approach be considered in patients with Morquio syndrome undergoing general anaesthesia. BioMed Central 2010-02-26 /pmc/articles/PMC2841068/ /pubmed/20184780 http://dx.doi.org/10.1186/1471-2253-10-2 Text en Copyright ©2010 McLaughlin et al; licensee BioMed Central Ltd. http://creativecommons.org/licenses/by/2.0 This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/2.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case report
McLaughlin, Anne Marie
Farooq, Muhammad
Donnelly, Maria B
Foley, Kieran
Anaesthetic considerations of adults with Morquio's syndrome - a case report
title Anaesthetic considerations of adults with Morquio's syndrome - a case report
title_full Anaesthetic considerations of adults with Morquio's syndrome - a case report
title_fullStr Anaesthetic considerations of adults with Morquio's syndrome - a case report
title_full_unstemmed Anaesthetic considerations of adults with Morquio's syndrome - a case report
title_short Anaesthetic considerations of adults with Morquio's syndrome - a case report
title_sort anaesthetic considerations of adults with morquio's syndrome - a case report
topic Case report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2841068/
https://www.ncbi.nlm.nih.gov/pubmed/20184780
http://dx.doi.org/10.1186/1471-2253-10-2
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AT farooqmuhammad anaestheticconsiderationsofadultswithmorquiossyndromeacasereport
AT donnellymariab anaestheticconsiderationsofadultswithmorquiossyndromeacasereport
AT foleykieran anaestheticconsiderationsofadultswithmorquiossyndromeacasereport

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