A Rare Cause of Heart Failure Treated by Heart Transplantation: Noncompaction of the Ventricular Myocardium

Noncompaction of the ventricular myocardium is a rare cardiomyopathy due to an arrest of myocardial morphogenesis. The characteristic echocardiographic findings are prominent myocardial trabeculations and deep intertrabecular spaces communicating with the left ventricular cavity. The clinical manife...

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Detalles Bibliográficos
Autores principales: Bordes, Julien, Jop, Bertrand, Imbert, Sandrine, Hraiech, Sami, Collard, Frédéric, Kerbaul, François
Formato: Texto
Lenguaje:English
Publicado: Hindawi Publishing Corporation 2009
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2842893/
https://www.ncbi.nlm.nih.gov/pubmed/20339508
http://dx.doi.org/10.1155/2009/725879
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author Bordes, Julien
Jop, Bertrand
Imbert, Sandrine
Hraiech, Sami
Collard, Frédéric
Kerbaul, François
author_facet Bordes, Julien
Jop, Bertrand
Imbert, Sandrine
Hraiech, Sami
Collard, Frédéric
Kerbaul, François
author_sort Bordes, Julien
collection PubMed
description Noncompaction of the ventricular myocardium is a rare cardiomyopathy due to an arrest of myocardial morphogenesis. The characteristic echocardiographic findings are prominent myocardial trabeculations and deep intertrabecular spaces communicating with the left ventricular cavity. The clinical manifestations include heart failure (HF) signs, ventricular arrhythmias, and cardioembolic events. We describe an illustrative case of noncompaction of the ventricular myocardium associated with bicuspid aortic valve, a 42-year-old male presenting a refractory acute heart failure successfully treated by emergency heart transplantation.
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spelling pubmed-28428932010-03-25 A Rare Cause of Heart Failure Treated by Heart Transplantation: Noncompaction of the Ventricular Myocardium Bordes, Julien Jop, Bertrand Imbert, Sandrine Hraiech, Sami Collard, Frédéric Kerbaul, François Case Rep Med Case Report Noncompaction of the ventricular myocardium is a rare cardiomyopathy due to an arrest of myocardial morphogenesis. The characteristic echocardiographic findings are prominent myocardial trabeculations and deep intertrabecular spaces communicating with the left ventricular cavity. The clinical manifestations include heart failure (HF) signs, ventricular arrhythmias, and cardioembolic events. We describe an illustrative case of noncompaction of the ventricular myocardium associated with bicuspid aortic valve, a 42-year-old male presenting a refractory acute heart failure successfully treated by emergency heart transplantation. Hindawi Publishing Corporation 2009 2010-03-18 /pmc/articles/PMC2842893/ /pubmed/20339508 http://dx.doi.org/10.1155/2009/725879 Text en Copyright © 2009 Julien Bordes et al. https://creativecommons.org/licenses/by/3.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Bordes, Julien
Jop, Bertrand
Imbert, Sandrine
Hraiech, Sami
Collard, Frédéric
Kerbaul, François
A Rare Cause of Heart Failure Treated by Heart Transplantation: Noncompaction of the Ventricular Myocardium
title A Rare Cause of Heart Failure Treated by Heart Transplantation: Noncompaction of the Ventricular Myocardium
title_full A Rare Cause of Heart Failure Treated by Heart Transplantation: Noncompaction of the Ventricular Myocardium
title_fullStr A Rare Cause of Heart Failure Treated by Heart Transplantation: Noncompaction of the Ventricular Myocardium
title_full_unstemmed A Rare Cause of Heart Failure Treated by Heart Transplantation: Noncompaction of the Ventricular Myocardium
title_short A Rare Cause of Heart Failure Treated by Heart Transplantation: Noncompaction of the Ventricular Myocardium
title_sort rare cause of heart failure treated by heart transplantation: noncompaction of the ventricular myocardium
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2842893/
https://www.ncbi.nlm.nih.gov/pubmed/20339508
http://dx.doi.org/10.1155/2009/725879
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