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Osteopetrosis with Micro-lacunar Resorption due to Defective Integrin Organization
We used in vitro differentiation of monocytes to characterize the cellular defect in a type of osteopetrosis with minimally functional osteoclasts, where defects associated with common causes of osteopetrosis were excluded by gene sequencing. Monocytes from blood of a 28 year old subject were differ...
Autores principales: | Blair, Harry C, Yaroslavskiy, Beatrice B, Robinson, Lisa J, Mapara, Markus Y, Pangrazio, Alessandra, Guo, Lida, Chen, Ka, Vezzoni, Paolo, Tolar, Jakub, Orchard, Paul J |
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Formato: | Texto |
Lenguaje: | English |
Publicado: |
2009
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2856930/ https://www.ncbi.nlm.nih.gov/pubmed/19546854 http://dx.doi.org/10.1038/labinvest.2009.58 |
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