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Massive hemoptysis and deep venous thrombosis presenting in a woman with Hughes-Stovin syndrome: a case report

INTRODUCTION: Hughes-Stovin syndrome is a very rare disease with fewer than 30 cases reported in the literature. The disease is thought to be a variant of Behcet's disease and is defined by the presence of pulmonary artery aneurysm in association with peripheral venous thrombosis. CASE PRESENTA...

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Autor principal: Al-Jahdali, Hamdan
Formato: Texto
Lenguaje:English
Publicado: BioMed Central 2010
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2864281/
https://www.ncbi.nlm.nih.gov/pubmed/20409300
http://dx.doi.org/10.1186/1752-1947-4-109
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author Al-Jahdali, Hamdan
author_facet Al-Jahdali, Hamdan
author_sort Al-Jahdali, Hamdan
collection PubMed
description INTRODUCTION: Hughes-Stovin syndrome is a very rare disease with fewer than 30 cases reported in the literature. The disease is thought to be a variant of Behcet's disease and is defined by the presence of pulmonary artery aneurysm in association with peripheral venous thrombosis. CASE PRESENTATION: A previously healthy 23-year-old Saudi woman presented with massive hemoptysis a day prior to her admission to our hospital. She had a six-month history of recurrent fever, cough, dyspnea, and recurrent oral ulceration. Contrast-enhanced computed tomography scan of her chest and pulmonary angiogram demonstrated a single right-lower lobe pulmonary artery aneurysm. She underwent thoracotomy and right lower lobe resection. Her postoperative course was complicated by deep vein thrombosis. She also developed headache and papilledema, while a magnetic resonance imaging of her brain suggested vasculitis. Based on these clinical presentations, she was diagnosed and treated with Hughes-Stovin syndrome. CONCLUSION: The majority of cases of Hughes-Stovin syndrome are reported among men, with only two cases occurring in women. A case of Hughes-Stovin syndrome occurring in a woman is presented in this report. She was treated successfully with multimodality treatment that includes surgery, steroids and cytotoxic agents.
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spelling pubmed-28642812010-05-05 Massive hemoptysis and deep venous thrombosis presenting in a woman with Hughes-Stovin syndrome: a case report Al-Jahdali, Hamdan J Med Case Reports Case report INTRODUCTION: Hughes-Stovin syndrome is a very rare disease with fewer than 30 cases reported in the literature. The disease is thought to be a variant of Behcet's disease and is defined by the presence of pulmonary artery aneurysm in association with peripheral venous thrombosis. CASE PRESENTATION: A previously healthy 23-year-old Saudi woman presented with massive hemoptysis a day prior to her admission to our hospital. She had a six-month history of recurrent fever, cough, dyspnea, and recurrent oral ulceration. Contrast-enhanced computed tomography scan of her chest and pulmonary angiogram demonstrated a single right-lower lobe pulmonary artery aneurysm. She underwent thoracotomy and right lower lobe resection. Her postoperative course was complicated by deep vein thrombosis. She also developed headache and papilledema, while a magnetic resonance imaging of her brain suggested vasculitis. Based on these clinical presentations, she was diagnosed and treated with Hughes-Stovin syndrome. CONCLUSION: The majority of cases of Hughes-Stovin syndrome are reported among men, with only two cases occurring in women. A case of Hughes-Stovin syndrome occurring in a woman is presented in this report. She was treated successfully with multimodality treatment that includes surgery, steroids and cytotoxic agents. BioMed Central 2010-04-21 /pmc/articles/PMC2864281/ /pubmed/20409300 http://dx.doi.org/10.1186/1752-1947-4-109 Text en Copyright ©2010 Al-Jahdali; licensee BioMed Central Ltd. http://creativecommons.org/licenses/by/2.0 This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/2.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case report
Al-Jahdali, Hamdan
Massive hemoptysis and deep venous thrombosis presenting in a woman with Hughes-Stovin syndrome: a case report
title Massive hemoptysis and deep venous thrombosis presenting in a woman with Hughes-Stovin syndrome: a case report
title_full Massive hemoptysis and deep venous thrombosis presenting in a woman with Hughes-Stovin syndrome: a case report
title_fullStr Massive hemoptysis and deep venous thrombosis presenting in a woman with Hughes-Stovin syndrome: a case report
title_full_unstemmed Massive hemoptysis and deep venous thrombosis presenting in a woman with Hughes-Stovin syndrome: a case report
title_short Massive hemoptysis and deep venous thrombosis presenting in a woman with Hughes-Stovin syndrome: a case report
title_sort massive hemoptysis and deep venous thrombosis presenting in a woman with hughes-stovin syndrome: a case report
topic Case report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2864281/
https://www.ncbi.nlm.nih.gov/pubmed/20409300
http://dx.doi.org/10.1186/1752-1947-4-109
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