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Survival in severe alpha-1-antitrypsin deficiency (PiZZ)

BACKGROUND: Previous studies of the natural history of alpha-1-antitrypsin (AAT) deficiency are mostly based on highly selected patients. The aim of this study was to analyse the mortality of PiZZ individuals. METHODS: Data from 1339 adult PiZZ individuals from the Swedish National AAT Deficiency Re...

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Detalles Bibliográficos
Autores principales:	Tanash, Hanan A, Nilsson, Peter M, Nilsson, Jan-Åke, Piitulainen, Eeva
Formato:	Texto
Lenguaje:	English
Publicado:	BioMed Central 2010
Materias:	Research
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2867977/ https://www.ncbi.nlm.nih.gov/pubmed/20420704 http://dx.doi.org/10.1186/1465-9921-11-44

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