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Patient-recorded outcome to assess therapeutic efficacy in protoporphyria-induced dermal phototoxicity: a proposal
BACKGROUND: Protoporphyria (PP) resulting from two rare, inherited diseases of heme biosynthesis leads to dermal phototoxicity by accumulation of the heme precursor protoporphyrin IX. No standardized tools to quantify the degree of PP-related phototoxicity and its change by medical intervention have...
Autores principales: | Minder, Elisabeth I, Schneider-Yin, Xiaoye, Minder, Christoph E |
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Formato: | Texto |
Lenguaje: | English |
Publicado: |
BioMed Central
2010
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2905349/ https://www.ncbi.nlm.nih.gov/pubmed/20565969 http://dx.doi.org/10.1186/1477-7525-8-60 |
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