Epithelioid Angiosarcoma in a Patient with Klippel-Trénaunay-Weber Syndrome: An Unexpected Response to Therapy

We present a rare case of Stewart-Treves syndrome characterized by a diffuse angiosarcoma of the leg in a 22-year-old man with a history of chronic lymphedema due to Klippel-Trénaunay-Weber syndrome. He underwent limb disarticulation and medical treatment with cycles of doxorubicin, oral thalidomide...

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Detalles Bibliográficos
Autores principales: Simas, Ângela, Matos, Catarina, Lopes da Silva, Rodrigo, Brotas, Vítor, Teófilo, Eugénio, Albino, José Pereira
Formato: Texto
Lenguaje:English
Publicado: S. Karger AG 2010
Materias:
Published: April 2010
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2919991/
https://www.ncbi.nlm.nih.gov/pubmed/20740188
http://dx.doi.org/10.1159/000313990
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author Simas, Ângela
Matos, Catarina
Lopes da Silva, Rodrigo
Brotas, Vítor
Teófilo, Eugénio
Albino, José Pereira
author_facet Simas, Ângela
Matos, Catarina
Lopes da Silva, Rodrigo
Brotas, Vítor
Teófilo, Eugénio
Albino, José Pereira
author_sort Simas, Ângela
collection PubMed
description We present a rare case of Stewart-Treves syndrome characterized by a diffuse angiosarcoma of the leg in a 22-year-old man with a history of chronic lymphedema due to Klippel-Trénaunay-Weber syndrome. He underwent limb disarticulation and medical treatment with cycles of doxorubicin, oral thalidomide and sunitinib with a very good response after 12 months of follow-up.
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spelling pubmed-29199912010-08-25 Epithelioid Angiosarcoma in a Patient with Klippel-Trénaunay-Weber Syndrome: An Unexpected Response to Therapy Simas, Ângela Matos, Catarina Lopes da Silva, Rodrigo Brotas, Vítor Teófilo, Eugénio Albino, José Pereira Case Rep Oncol Published: April 2010 We present a rare case of Stewart-Treves syndrome characterized by a diffuse angiosarcoma of the leg in a 22-year-old man with a history of chronic lymphedema due to Klippel-Trénaunay-Weber syndrome. He underwent limb disarticulation and medical treatment with cycles of doxorubicin, oral thalidomide and sunitinib with a very good response after 12 months of follow-up. S. Karger AG 2010-04-30 /pmc/articles/PMC2919991/ /pubmed/20740188 http://dx.doi.org/10.1159/000313990 Text en Copyright © 2010 by S. Karger AG, Basel http://creativecommons.org/licenses/by-nc-nd/3.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution-Noncommercial-No-Derivative-Works License (http://creativecommons.org/licenses/by-nc-nd/3.0/). Users may download, print and share this work on the Internet for noncommercial purposes only, provided the original work is properly cited, and a link to the original work on http://www.karger.com and the terms of this license are included in any shared versions.
spellingShingle Published: April 2010
Simas, Ângela
Matos, Catarina
Lopes da Silva, Rodrigo
Brotas, Vítor
Teófilo, Eugénio
Albino, José Pereira
Epithelioid Angiosarcoma in a Patient with Klippel-Trénaunay-Weber Syndrome: An Unexpected Response to Therapy
title Epithelioid Angiosarcoma in a Patient with Klippel-Trénaunay-Weber Syndrome: An Unexpected Response to Therapy
title_full Epithelioid Angiosarcoma in a Patient with Klippel-Trénaunay-Weber Syndrome: An Unexpected Response to Therapy
title_fullStr Epithelioid Angiosarcoma in a Patient with Klippel-Trénaunay-Weber Syndrome: An Unexpected Response to Therapy
title_full_unstemmed Epithelioid Angiosarcoma in a Patient with Klippel-Trénaunay-Weber Syndrome: An Unexpected Response to Therapy
title_short Epithelioid Angiosarcoma in a Patient with Klippel-Trénaunay-Weber Syndrome: An Unexpected Response to Therapy
title_sort epithelioid angiosarcoma in a patient with klippel-trénaunay-weber syndrome: an unexpected response to therapy
topic Published: April 2010
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2919991/
https://www.ncbi.nlm.nih.gov/pubmed/20740188
http://dx.doi.org/10.1159/000313990
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