Cargando…
Sclerosing cholangitis associated with retroperitoneal fibrosis: a case of multisystem fibroinflammatory disorder
INTRODUCTION: Retroperitoneal fibrosis is a fibroinflammatory disease of unknown etiology that can be associated with other fibroinflammatory disorders. Lately, there have been several reports showing that retroperitoneal fibrosis is a manifestation of IgG4-related sclerosing disease, which often pr...
Autores principales: | , , , , , |
---|---|
Formato: | Texto |
Lenguaje: | English |
Publicado: |
Springer-Verlag
2010
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2978902/ https://www.ncbi.nlm.nih.gov/pubmed/21286351 http://dx.doi.org/10.1007/s12072-010-9222-2 |
_version_ | 1782191317781053440 |
---|---|
author | Rompa, Grazyna T. Jablonska, Anna K. Guzek, Marek T. Dubowik, Michal M. Marek, Iwona E. Smoczynski, Marian K. |
author_facet | Rompa, Grazyna T. Jablonska, Anna K. Guzek, Marek T. Dubowik, Michal M. Marek, Iwona E. Smoczynski, Marian K. |
author_sort | Rompa, Grazyna T. |
collection | PubMed |
description | INTRODUCTION: Retroperitoneal fibrosis is a fibroinflammatory disease of unknown etiology that can be associated with other fibroinflammatory disorders. Lately, there have been several reports showing that retroperitoneal fibrosis is a manifestation of IgG4-related sclerosing disease, which often presents as autoimmune pancreatitis. CASE REPORT: This report shows the case of IgG4-related sclerosing cholangitis associated with retroperitoneal fibrosis independent of autoimmune pancreatitis. The patient presented with cholestatic jaundice and picture of sclerosing cholangitis in endoscopic retrograde cholangiography. The combination of endoscopic biliary drainage and steroid therapy was an effective treatment in this case. CONCLUSION: The diagnosis of IgG4-related sclerosing disease should always be taken into consideration in patients with sclerosing cholangitis, especially when it is associated with any fibroinflammatory disorder. |
format | Text |
id | pubmed-2978902 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2010 |
publisher | Springer-Verlag |
record_format | MEDLINE/PubMed |
spelling | pubmed-29789022010-12-08 Sclerosing cholangitis associated with retroperitoneal fibrosis: a case of multisystem fibroinflammatory disorder Rompa, Grazyna T. Jablonska, Anna K. Guzek, Marek T. Dubowik, Michal M. Marek, Iwona E. Smoczynski, Marian K. Hepatol Int Case Report INTRODUCTION: Retroperitoneal fibrosis is a fibroinflammatory disease of unknown etiology that can be associated with other fibroinflammatory disorders. Lately, there have been several reports showing that retroperitoneal fibrosis is a manifestation of IgG4-related sclerosing disease, which often presents as autoimmune pancreatitis. CASE REPORT: This report shows the case of IgG4-related sclerosing cholangitis associated with retroperitoneal fibrosis independent of autoimmune pancreatitis. The patient presented with cholestatic jaundice and picture of sclerosing cholangitis in endoscopic retrograde cholangiography. The combination of endoscopic biliary drainage and steroid therapy was an effective treatment in this case. CONCLUSION: The diagnosis of IgG4-related sclerosing disease should always be taken into consideration in patients with sclerosing cholangitis, especially when it is associated with any fibroinflammatory disorder. Springer-Verlag 2010-10-07 /pmc/articles/PMC2978902/ /pubmed/21286351 http://dx.doi.org/10.1007/s12072-010-9222-2 Text en © The Author(s) 2010 https://creativecommons.org/licenses/by-nc/4.0/ This article is distributed under the terms of the Creative Commons Attribution Noncommercial License which permits any noncommercial use, distribution, and reproduction in any medium, provided the original author(s) and source are credited. |
spellingShingle | Case Report Rompa, Grazyna T. Jablonska, Anna K. Guzek, Marek T. Dubowik, Michal M. Marek, Iwona E. Smoczynski, Marian K. Sclerosing cholangitis associated with retroperitoneal fibrosis: a case of multisystem fibroinflammatory disorder |
title | Sclerosing cholangitis associated with retroperitoneal fibrosis: a case of multisystem fibroinflammatory disorder |
title_full | Sclerosing cholangitis associated with retroperitoneal fibrosis: a case of multisystem fibroinflammatory disorder |
title_fullStr | Sclerosing cholangitis associated with retroperitoneal fibrosis: a case of multisystem fibroinflammatory disorder |
title_full_unstemmed | Sclerosing cholangitis associated with retroperitoneal fibrosis: a case of multisystem fibroinflammatory disorder |
title_short | Sclerosing cholangitis associated with retroperitoneal fibrosis: a case of multisystem fibroinflammatory disorder |
title_sort | sclerosing cholangitis associated with retroperitoneal fibrosis: a case of multisystem fibroinflammatory disorder |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2978902/ https://www.ncbi.nlm.nih.gov/pubmed/21286351 http://dx.doi.org/10.1007/s12072-010-9222-2 |
work_keys_str_mv | AT rompagrazynat sclerosingcholangitisassociatedwithretroperitonealfibrosisacaseofmultisystemfibroinflammatorydisorder AT jablonskaannak sclerosingcholangitisassociatedwithretroperitonealfibrosisacaseofmultisystemfibroinflammatorydisorder AT guzekmarekt sclerosingcholangitisassociatedwithretroperitonealfibrosisacaseofmultisystemfibroinflammatorydisorder AT dubowikmichalm sclerosingcholangitisassociatedwithretroperitonealfibrosisacaseofmultisystemfibroinflammatorydisorder AT marekiwonae sclerosingcholangitisassociatedwithretroperitonealfibrosisacaseofmultisystemfibroinflammatorydisorder AT smoczynskimariank sclerosingcholangitisassociatedwithretroperitonealfibrosisacaseofmultisystemfibroinflammatorydisorder |