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Scimitar syndrome and evolution of managements

The Scimitar syndrome is a rare congenital anomaly that consists in part of total or partial anomalous venous drainage of the right lung to the inferior vena cava (IVC). This descending vein is visible on CXR as a curvilinear density along the right heart border and resembles the curved Turkish swor...

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Detalles Bibliográficos
Autores principales: Kahrom, Mahdi, Kahrom, Hadi
Formato: Texto
Lenguaje:English
Publicado: African Field Epidemiology Network 2009
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2984288/
https://www.ncbi.nlm.nih.gov/pubmed/21532729
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author Kahrom, Mahdi
Kahrom, Hadi
author_facet Kahrom, Mahdi
Kahrom, Hadi
author_sort Kahrom, Mahdi
collection PubMed
description The Scimitar syndrome is a rare congenital anomaly that consists in part of total or partial anomalous venous drainage of the right lung to the inferior vena cava (IVC). This descending vein is visible on CXR as a curvilinear density along the right heart border and resembles the curved Turkish sword that gives the condition its name. Scimitar syndrome forms part of the large spectrum of associated conditions known as venolobar syndrome. These include right lung hypoplasia or sequestered segments of the right lung, congenital heart disease and various others. Surgical approaches to the Scimitar syndrome have varied according to the anatomic and pathologic features presented in each case. Here we review the clinical signs and symptoms, diagnostic dilemmas, current medical and surgical managements of Scimitar syndrome.
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spelling pubmed-29842882010-11-30 Scimitar syndrome and evolution of managements Kahrom, Mahdi Kahrom, Hadi Pan Afr Med J Review The Scimitar syndrome is a rare congenital anomaly that consists in part of total or partial anomalous venous drainage of the right lung to the inferior vena cava (IVC). This descending vein is visible on CXR as a curvilinear density along the right heart border and resembles the curved Turkish sword that gives the condition its name. Scimitar syndrome forms part of the large spectrum of associated conditions known as venolobar syndrome. These include right lung hypoplasia or sequestered segments of the right lung, congenital heart disease and various others. Surgical approaches to the Scimitar syndrome have varied according to the anatomic and pathologic features presented in each case. Here we review the clinical signs and symptoms, diagnostic dilemmas, current medical and surgical managements of Scimitar syndrome. African Field Epidemiology Network 2009-12-17 /pmc/articles/PMC2984288/ /pubmed/21532729 Text en Copyright © 2009 Mahdi Kahrom et al http://creativecommons.org/licenses/by/2.0/ The Pan African Medical Journal - ISSN 1937-8688. This is an Open Access article distributed under the terms of the Creative Commons Attribution License which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Review
Kahrom, Mahdi
Kahrom, Hadi
Scimitar syndrome and evolution of managements
title Scimitar syndrome and evolution of managements
title_full Scimitar syndrome and evolution of managements
title_fullStr Scimitar syndrome and evolution of managements
title_full_unstemmed Scimitar syndrome and evolution of managements
title_short Scimitar syndrome and evolution of managements
title_sort scimitar syndrome and evolution of managements
topic Review
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2984288/
https://www.ncbi.nlm.nih.gov/pubmed/21532729
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