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Congenital infantile digital fibromatosis: a case report and review of the literature

Infantile digital fibromatosis (IDF) is a rare benign fibroproliferative tumor of early childhood. IDF preferentially affects the fingers and the toes. Malignant transformation or metastases have never been reported. Surgical treatment has been advocated previously but local recurrences were observe...

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Autores principales: Failla, Valérie, Wauters, Odile, Nikkels-Tassoudji, Nazli, Carlier, Alain, André, Josette, Nikkels, Arjen F
Formato: Texto
Lenguaje:English
Publicado: PAGEPress Publications 2009
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2994462/
https://www.ncbi.nlm.nih.gov/pubmed/21139926
http://dx.doi.org/10.4081/rt.2009.e47
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author Failla, Valérie
Wauters, Odile
Nikkels-Tassoudji, Nazli
Carlier, Alain
André, Josette
Nikkels, Arjen F
author_facet Failla, Valérie
Wauters, Odile
Nikkels-Tassoudji, Nazli
Carlier, Alain
André, Josette
Nikkels, Arjen F
author_sort Failla, Valérie
collection PubMed
description Infantile digital fibromatosis (IDF) is a rare benign fibroproliferative tumor of early childhood. IDF preferentially affects the fingers and the toes. Malignant transformation or metastases have never been reported. Surgical treatment has been advocated previously but local recurrences were observed frequently. Recent literature supports clinical surveillance without any medical or surgical intervention as spontaneous regression usually occurs after two to three years. A six-month-old Caucasian girl with IDF on the left fourth digit is presented here. The tumor progressively increased in size after birth. Topical imiquimod cream and diflucortolone valerate cream, both displaying antifibrotic properties, had no effect on tumor growth. Currently the lesion size remains stable without any treatment. Early recognition of IDF is important in order to avoid unnecessary surgical intervention that may prove to be potentially aggravating, unless serious functional or cosmetic concerns intervene. Parents should be reassured concerning the benign nature of IDF and be informed that spontaneous involution of IDF might be expected.
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spelling pubmed-29944622010-12-07 Congenital infantile digital fibromatosis: a case report and review of the literature Failla, Valérie Wauters, Odile Nikkels-Tassoudji, Nazli Carlier, Alain André, Josette Nikkels, Arjen F Rare Tumors Case Report Infantile digital fibromatosis (IDF) is a rare benign fibroproliferative tumor of early childhood. IDF preferentially affects the fingers and the toes. Malignant transformation or metastases have never been reported. Surgical treatment has been advocated previously but local recurrences were observed frequently. Recent literature supports clinical surveillance without any medical or surgical intervention as spontaneous regression usually occurs after two to three years. A six-month-old Caucasian girl with IDF on the left fourth digit is presented here. The tumor progressively increased in size after birth. Topical imiquimod cream and diflucortolone valerate cream, both displaying antifibrotic properties, had no effect on tumor growth. Currently the lesion size remains stable without any treatment. Early recognition of IDF is important in order to avoid unnecessary surgical intervention that may prove to be potentially aggravating, unless serious functional or cosmetic concerns intervene. Parents should be reassured concerning the benign nature of IDF and be informed that spontaneous involution of IDF might be expected. PAGEPress Publications 2009-12-28 /pmc/articles/PMC2994462/ /pubmed/21139926 http://dx.doi.org/10.4081/rt.2009.e47 Text en ©Copyright V. Failla et al.,2009 This work is licensed under a Creative Commons Attribution 3.0 License (by-nc 3.0). Licensee PAGEPress, Italy
spellingShingle Case Report
Failla, Valérie
Wauters, Odile
Nikkels-Tassoudji, Nazli
Carlier, Alain
André, Josette
Nikkels, Arjen F
Congenital infantile digital fibromatosis: a case report and review of the literature
title Congenital infantile digital fibromatosis: a case report and review of the literature
title_full Congenital infantile digital fibromatosis: a case report and review of the literature
title_fullStr Congenital infantile digital fibromatosis: a case report and review of the literature
title_full_unstemmed Congenital infantile digital fibromatosis: a case report and review of the literature
title_short Congenital infantile digital fibromatosis: a case report and review of the literature
title_sort congenital infantile digital fibromatosis: a case report and review of the literature
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2994462/
https://www.ncbi.nlm.nih.gov/pubmed/21139926
http://dx.doi.org/10.4081/rt.2009.e47
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