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Cystic fibrohistiocytic tumor of the lung presenting as a solitary lesion
Cystic fibrohistiocytic tumor of the lung is a rare neoplasm. In many cases it represents a metastasis from a benign or low-grade fibrohistiocytic tumor of the skin, but occasionally it may be primary. Radiologically it usually occurs as a cystic change of multiple pulmonary nodules, and pneumothora...
Autores principales: | , , , , , |
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Formato: | Texto |
Lenguaje: | English |
Publicado: |
PagePress
2010
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2994490/ https://www.ncbi.nlm.nih.gov/pubmed/21139943 http://dx.doi.org/10.4081/rt.2010.e14 |
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author | Paci, Massimiliano Cavazza, Alberto Annessi, Valerio Ricchetti, Tommaso Rapicetta, Cristian Sgarbi, Giorgio |
author_facet | Paci, Massimiliano Cavazza, Alberto Annessi, Valerio Ricchetti, Tommaso Rapicetta, Cristian Sgarbi, Giorgio |
author_sort | Paci, Massimiliano |
collection | PubMed |
description | Cystic fibrohistiocytic tumor of the lung is a rare neoplasm. In many cases it represents a metastasis from a benign or low-grade fibrohistiocytic tumor of the skin, but occasionally it may be primary. Radiologically it usually occurs as a cystic change of multiple pulmonary nodules, and pneumothorax is the most frequent presenting symptom. We present here a 16-year-old man with recurrent right pneumothorax. The patient had no history of cutaneous fibrohistiocytic lesions. He underwent videothoracoscopic right apical segmentectomy, right lower lobe nodulectomy, and pleuroabrasion. Microscopy of the apical segmentectomy showed a cystic fibrohistiocytic tumor, whereas the nodule of the lower lobe was an intraparenchymal lymph node. The patient is alive with no tumor recurrence. The differential diagnosis includes Langerhans cell histiocytosis, lymphangioleiomyomatosis, pleuropulmonary blastoma, and metastatic endometrial stromal sarcoma. This disease usually occurs with multiple pulmonary cysts and cavitation. This case is the first reported presenting as a single lesion. |
format | Text |
id | pubmed-2994490 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2010 |
publisher | PagePress |
record_format | MEDLINE/PubMed |
spelling | pubmed-29944902010-12-07 Cystic fibrohistiocytic tumor of the lung presenting as a solitary lesion Paci, Massimiliano Cavazza, Alberto Annessi, Valerio Ricchetti, Tommaso Rapicetta, Cristian Sgarbi, Giorgio Rare Tumors Case Report Cystic fibrohistiocytic tumor of the lung is a rare neoplasm. In many cases it represents a metastasis from a benign or low-grade fibrohistiocytic tumor of the skin, but occasionally it may be primary. Radiologically it usually occurs as a cystic change of multiple pulmonary nodules, and pneumothorax is the most frequent presenting symptom. We present here a 16-year-old man with recurrent right pneumothorax. The patient had no history of cutaneous fibrohistiocytic lesions. He underwent videothoracoscopic right apical segmentectomy, right lower lobe nodulectomy, and pleuroabrasion. Microscopy of the apical segmentectomy showed a cystic fibrohistiocytic tumor, whereas the nodule of the lower lobe was an intraparenchymal lymph node. The patient is alive with no tumor recurrence. The differential diagnosis includes Langerhans cell histiocytosis, lymphangioleiomyomatosis, pleuropulmonary blastoma, and metastatic endometrial stromal sarcoma. This disease usually occurs with multiple pulmonary cysts and cavitation. This case is the first reported presenting as a single lesion. PagePress 2010-03-31 /pmc/articles/PMC2994490/ /pubmed/21139943 http://dx.doi.org/10.4081/rt.2010.e14 Text en ©Copyright M. Paci et al., 2010 This work is licensed under a Creative Commons Attribution 3.0 License (by-nc 3.0). Licensee PAGEPress, Italy |
spellingShingle | Case Report Paci, Massimiliano Cavazza, Alberto Annessi, Valerio Ricchetti, Tommaso Rapicetta, Cristian Sgarbi, Giorgio Cystic fibrohistiocytic tumor of the lung presenting as a solitary lesion |
title | Cystic fibrohistiocytic tumor of the lung presenting as a solitary lesion |
title_full | Cystic fibrohistiocytic tumor of the lung presenting as a solitary lesion |
title_fullStr | Cystic fibrohistiocytic tumor of the lung presenting as a solitary lesion |
title_full_unstemmed | Cystic fibrohistiocytic tumor of the lung presenting as a solitary lesion |
title_short | Cystic fibrohistiocytic tumor of the lung presenting as a solitary lesion |
title_sort | cystic fibrohistiocytic tumor of the lung presenting as a solitary lesion |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2994490/ https://www.ncbi.nlm.nih.gov/pubmed/21139943 http://dx.doi.org/10.4081/rt.2010.e14 |
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