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A Case of Isolated Left Ventricular Noncompaction with Basal ECG-Tracing Strongly Suggestive for Type-2 Brugada Syndrome

Isolated left ventricular noncompaction (ILVNC) is a cardiomyopathy caused by intrauterine arrest of compaction of the myocardial fibres and meshwork, an important process in myocardial development. ILVNC is clinically accompanied by depressed ventricular function, arrhythmias, and systemic emboliza...

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Autores principales: Banci, Maria, Martinoli, Roberta, Dofcaci, Alessandro, Piccirilli, Stefano, Papetti, Federica, Sansoni, Ilaria, Saccucci, Patrizia
Formato: Texto
Lenguaje:English
Publicado: SAGE-Hindawi Access to Research 2010
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2995903/
https://www.ncbi.nlm.nih.gov/pubmed/21151698
http://dx.doi.org/10.4061/2011/201962
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author Banci, Maria
Martinoli, Roberta
Dofcaci, Alessandro
Piccirilli, Stefano
Papetti, Federica
Sansoni, Ilaria
Saccucci, Patrizia
author_facet Banci, Maria
Martinoli, Roberta
Dofcaci, Alessandro
Piccirilli, Stefano
Papetti, Federica
Sansoni, Ilaria
Saccucci, Patrizia
author_sort Banci, Maria
collection PubMed
description Isolated left ventricular noncompaction (ILVNC) is a cardiomyopathy caused by intrauterine arrest of compaction of the myocardial fibres and meshwork, an important process in myocardial development. ILVNC is clinically accompanied by depressed ventricular function, arrhythmias, and systemic embolization. We reported a case of ILVNC with basal ECG-tracing strongly suggestive for type-2 Brugada syndrome (BrS). Up to now, this is the first report investigating the association between ILVNC and this particular ECG pattern.
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spelling pubmed-29959032010-12-13 A Case of Isolated Left Ventricular Noncompaction with Basal ECG-Tracing Strongly Suggestive for Type-2 Brugada Syndrome Banci, Maria Martinoli, Roberta Dofcaci, Alessandro Piccirilli, Stefano Papetti, Federica Sansoni, Ilaria Saccucci, Patrizia Cardiol Res Pract Case Report Isolated left ventricular noncompaction (ILVNC) is a cardiomyopathy caused by intrauterine arrest of compaction of the myocardial fibres and meshwork, an important process in myocardial development. ILVNC is clinically accompanied by depressed ventricular function, arrhythmias, and systemic embolization. We reported a case of ILVNC with basal ECG-tracing strongly suggestive for type-2 Brugada syndrome (BrS). Up to now, this is the first report investigating the association between ILVNC and this particular ECG pattern. SAGE-Hindawi Access to Research 2010-12-01 /pmc/articles/PMC2995903/ /pubmed/21151698 http://dx.doi.org/10.4061/2011/201962 Text en Copyright © 2011 Maria Banci et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Banci, Maria
Martinoli, Roberta
Dofcaci, Alessandro
Piccirilli, Stefano
Papetti, Federica
Sansoni, Ilaria
Saccucci, Patrizia
A Case of Isolated Left Ventricular Noncompaction with Basal ECG-Tracing Strongly Suggestive for Type-2 Brugada Syndrome
title A Case of Isolated Left Ventricular Noncompaction with Basal ECG-Tracing Strongly Suggestive for Type-2 Brugada Syndrome
title_full A Case of Isolated Left Ventricular Noncompaction with Basal ECG-Tracing Strongly Suggestive for Type-2 Brugada Syndrome
title_fullStr A Case of Isolated Left Ventricular Noncompaction with Basal ECG-Tracing Strongly Suggestive for Type-2 Brugada Syndrome
title_full_unstemmed A Case of Isolated Left Ventricular Noncompaction with Basal ECG-Tracing Strongly Suggestive for Type-2 Brugada Syndrome
title_short A Case of Isolated Left Ventricular Noncompaction with Basal ECG-Tracing Strongly Suggestive for Type-2 Brugada Syndrome
title_sort case of isolated left ventricular noncompaction with basal ecg-tracing strongly suggestive for type-2 brugada syndrome
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC2995903/
https://www.ncbi.nlm.nih.gov/pubmed/21151698
http://dx.doi.org/10.4061/2011/201962
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