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Laparoscopic Management of Small Bowel Intussusception in a 16-Year-Old With Peutz-Jeghers Syndrome

INTRODUCTION: Peutz-Jeghers is a rare autosomal dominant disorder characterized by hamartomatous polyps and discoloration of mucosal membranes. The polyps can occur anywhere in the gastrointestinal tract and can grow large enough to cause bowel obstructions. CASE REPORT: A 16-year-old male presented...

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Autores principales: Morales Gonzalez, Angel Mario, Clapp, Benjamin
Formato: Texto
Lenguaje:English
Publicado: Society of Laparoendoscopic Surgeons 2008
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3015883/
https://www.ncbi.nlm.nih.gov/pubmed/18765065
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author Morales Gonzalez, Angel Mario
Clapp, Benjamin
author_facet Morales Gonzalez, Angel Mario
Clapp, Benjamin
author_sort Morales Gonzalez, Angel Mario
collection PubMed
description INTRODUCTION: Peutz-Jeghers is a rare autosomal dominant disorder characterized by hamartomatous polyps and discoloration of mucosal membranes. The polyps can occur anywhere in the gastrointestinal tract and can grow large enough to cause bowel obstructions. CASE REPORT: A 16-year-old male presented to the emergency department with signs and symptoms of an acute bowel obstruction. He had 2 days of abdominal pain, obstipation, and vomiting. He had a previous history of a colonoscopy with polypectomy at age 4, and hyperpigmentation of his mucous membranes. RESULTS: Computed tomographic (CT) scan revealed an intussusception of the small intestine. An exploratory laparoscopy found an intussusception of the mid jejunum. A laparoscopic-assisted small bowel resection was performed. Pathology showed a 5-cm polyp that acted as a lead point for the intussusception. Colonoscopy and upper endoscopy revealed 5 more polyps in the stomach and colon that were removed. CONCLUSION: Small bowel obstructions can be managed successfully with minimally invasive approaches. The treatment of obstruction in these patients is to remove the offending hamartomatous polyp(s). The rest of the intestine needs to be examined and those polyps found should be removed. This can be done intraoperatively with laparoscopic-assisted enteroscopy and colonoscopy.
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spelling pubmed-30158832011-02-17 Laparoscopic Management of Small Bowel Intussusception in a 16-Year-Old With Peutz-Jeghers Syndrome Morales Gonzalez, Angel Mario Clapp, Benjamin JSLS Case Reports INTRODUCTION: Peutz-Jeghers is a rare autosomal dominant disorder characterized by hamartomatous polyps and discoloration of mucosal membranes. The polyps can occur anywhere in the gastrointestinal tract and can grow large enough to cause bowel obstructions. CASE REPORT: A 16-year-old male presented to the emergency department with signs and symptoms of an acute bowel obstruction. He had 2 days of abdominal pain, obstipation, and vomiting. He had a previous history of a colonoscopy with polypectomy at age 4, and hyperpigmentation of his mucous membranes. RESULTS: Computed tomographic (CT) scan revealed an intussusception of the small intestine. An exploratory laparoscopy found an intussusception of the mid jejunum. A laparoscopic-assisted small bowel resection was performed. Pathology showed a 5-cm polyp that acted as a lead point for the intussusception. Colonoscopy and upper endoscopy revealed 5 more polyps in the stomach and colon that were removed. CONCLUSION: Small bowel obstructions can be managed successfully with minimally invasive approaches. The treatment of obstruction in these patients is to remove the offending hamartomatous polyp(s). The rest of the intestine needs to be examined and those polyps found should be removed. This can be done intraoperatively with laparoscopic-assisted enteroscopy and colonoscopy. Society of Laparoendoscopic Surgeons 2008 /pmc/articles/PMC3015883/ /pubmed/18765065 Text en © 2008 by JSLS, Journal of the Society of Laparoendoscopic Surgeons This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial No Derivatives License (http://creativecommons.org/licenses/by-nc-nd/3.0/), which permits for noncommercial use, distribution, and reproduction in any medium, provided the original work is properly cited and is not altered in any way.
spellingShingle Case Reports
Morales Gonzalez, Angel Mario
Clapp, Benjamin
Laparoscopic Management of Small Bowel Intussusception in a 16-Year-Old With Peutz-Jeghers Syndrome
title Laparoscopic Management of Small Bowel Intussusception in a 16-Year-Old With Peutz-Jeghers Syndrome
title_full Laparoscopic Management of Small Bowel Intussusception in a 16-Year-Old With Peutz-Jeghers Syndrome
title_fullStr Laparoscopic Management of Small Bowel Intussusception in a 16-Year-Old With Peutz-Jeghers Syndrome
title_full_unstemmed Laparoscopic Management of Small Bowel Intussusception in a 16-Year-Old With Peutz-Jeghers Syndrome
title_short Laparoscopic Management of Small Bowel Intussusception in a 16-Year-Old With Peutz-Jeghers Syndrome
title_sort laparoscopic management of small bowel intussusception in a 16-year-old with peutz-jeghers syndrome
topic Case Reports
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3015883/
https://www.ncbi.nlm.nih.gov/pubmed/18765065
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