Budd-Chiari syndrome in a 25-year-old woman with Behçet's disease: a case report and review of the literature

INTRODUCTION: The risk that patients with Behçet's disease will develop thrombotic complications has been previously described. Although it is distributed worldwide, Behçet's disease is rare in the Americas and Europe. Even though the pathogenic mechanisms of vascular complications of Budd...

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Detalles Bibliográficos
Autores principales: Carvalho, Daniela T, Oikawa, Fernando T, Matsuda, Nilce M, Évora, Paulo RB, Yamada, Alice T
Formato: Texto
Lenguaje:English
Publicado: BioMed Central 2011
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3041762/
https://www.ncbi.nlm.nih.gov/pubmed/21299890
http://dx.doi.org/10.1186/1752-1947-5-52
Descripción
Sumario:INTRODUCTION: The risk that patients with Behçet's disease will develop thrombotic complications has been previously described. Although it is distributed worldwide, Behçet's disease is rare in the Americas and Europe. Even though the pathogenic mechanisms of vascular complications of Budd-Chiari syndrome in patients with Behçet's disease are unknown, severe vascular complications of Budd-Chiari syndrome associated with Behçet's disease seem to affect mainly young men. CASE PRESENTATION: We report a case of Budd-Chiari syndrome, a severe vascular complication that developed in a 25-year-old Afro-Brazilian woman with Behçet's disease. CONCLUSION: Severe vascular complications of Budd-Chiari syndrome in patients with Behçet's disease are much more common in young adult male patients; we present a rare case of Budd-Chiari syndrome in a young Afro-Brazilian woman with Behçet's disease.

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