Changes in Glycogen and Glycosaminoglycan Levels in Hepatocytes of Iduronate-2-Sulfatase Knockout Mice before and after Recombinant Iduronate-2-Sulfatase Supplementation

PURPOSE: Mucopolysaccharidosis II (MPS II) is a lysosomal storage disorder caused by a deficiency of iduronate-2 sulfatase (IdS), which is involved in the degradation of glycosaminoglycan (GAG). In this study, the frequency of fasting hypoglycemia in patients with MPS II was investigated and changes...

Descripción completa

Detalles Bibliográficos
Autores principales: Lee, Jee Hyun, Choe, Yon Ho, Kim, Su Jin, Paik, Kyung Hoon, Jin, Dong-Kyu
Formato: Texto
Lenguaje:English
Publicado: Yonsei University College of Medicine 2011
Materias:
Original Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3051226/
https://www.ncbi.nlm.nih.gov/pubmed/21319344
http://dx.doi.org/10.3349/ymj.2011.52.2.263

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3051226/
https://www.ncbi.nlm.nih.gov/pubmed/21319344
http://dx.doi.org/10.3349/ymj.2011.52.2.263

Ejemplares similares