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Chylothorax in Gorham's disease.

A 25-yr-old woman presented with a right pleural effusion. Destruction of 9th through 12th ribs, adjacent vertebral bodies, and transverse processes was noted on plain radiograph and a large low-attenuated, irregular shaped mass lesion with peripheral rim enhancement, destroying vertebral body and t...

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Autores principales: Lee, Won Sup, Kim, Sung Han, Kim, Inho, Kim, Hark Kyun, Lee, Keun Seok, Lee, Sang Yoon, Heo, Dae Seog, Jang, Bong-Soon, Bang, Yung-Jue, Kim, Noe Kyeong
Formato: Texto
Lenguaje:English
Publicado: Korean Academy of Medical Sciences 2002
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3054959/
https://www.ncbi.nlm.nih.gov/pubmed/12483010
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author Lee, Won Sup
Kim, Sung Han
Kim, Inho
Kim, Hark Kyun
Lee, Keun Seok
Lee, Sang Yoon
Heo, Dae Seog
Jang, Bong-Soon
Bang, Yung-Jue
Kim, Noe Kyeong
author_facet Lee, Won Sup
Kim, Sung Han
Kim, Inho
Kim, Hark Kyun
Lee, Keun Seok
Lee, Sang Yoon
Heo, Dae Seog
Jang, Bong-Soon
Bang, Yung-Jue
Kim, Noe Kyeong
author_sort Lee, Won Sup
collection PubMed
description A 25-yr-old woman presented with a right pleural effusion. Destruction of 9th through 12th ribs, adjacent vertebral bodies, and transverse processes was noted on plain radiograph and a large low-attenuated, irregular shaped mass lesion with peripheral rim enhancement, destroying vertebral body and transverse process, was revealed on the computed tomographic scan. Magnetic resonance imaging showed high signal on T1- weighted image and iso- and low signal on T2-weighted image for the mass lesion replacing the vertebral bony cortex and marrow space. An open rib biopsy revealed the histopathological changes of Gorham's disease (essential osteolysis), even though only bloody fluid filling the empty space and rib and vertebral transverse process destruction were grossly observed on operation. Even though there was no definite response to radiotherapy and pleurodesis, the patient showed stable condition up to 20 months after diagnosis.
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spelling pubmed-30549592011-03-15 Chylothorax in Gorham's disease. Lee, Won Sup Kim, Sung Han Kim, Inho Kim, Hark Kyun Lee, Keun Seok Lee, Sang Yoon Heo, Dae Seog Jang, Bong-Soon Bang, Yung-Jue Kim, Noe Kyeong J Korean Med Sci Research Article A 25-yr-old woman presented with a right pleural effusion. Destruction of 9th through 12th ribs, adjacent vertebral bodies, and transverse processes was noted on plain radiograph and a large low-attenuated, irregular shaped mass lesion with peripheral rim enhancement, destroying vertebral body and transverse process, was revealed on the computed tomographic scan. Magnetic resonance imaging showed high signal on T1- weighted image and iso- and low signal on T2-weighted image for the mass lesion replacing the vertebral bony cortex and marrow space. An open rib biopsy revealed the histopathological changes of Gorham's disease (essential osteolysis), even though only bloody fluid filling the empty space and rib and vertebral transverse process destruction were grossly observed on operation. Even though there was no definite response to radiotherapy and pleurodesis, the patient showed stable condition up to 20 months after diagnosis. Korean Academy of Medical Sciences 2002-12 /pmc/articles/PMC3054959/ /pubmed/12483010 Text en
spellingShingle Research Article
Lee, Won Sup
Kim, Sung Han
Kim, Inho
Kim, Hark Kyun
Lee, Keun Seok
Lee, Sang Yoon
Heo, Dae Seog
Jang, Bong-Soon
Bang, Yung-Jue
Kim, Noe Kyeong
Chylothorax in Gorham's disease.
title Chylothorax in Gorham's disease.
title_full Chylothorax in Gorham's disease.
title_fullStr Chylothorax in Gorham's disease.
title_full_unstemmed Chylothorax in Gorham's disease.
title_short Chylothorax in Gorham's disease.
title_sort chylothorax in gorham's disease.
topic Research Article
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3054959/
https://www.ncbi.nlm.nih.gov/pubmed/12483010
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