Septal agenesis and lissencephaly with colpocephaly presenting as the ‘Crown Sign’

Developmental malformations of the cortex in neuronal migration disorders result in constellation of findings on radiological scanning. Isolated defects are common but sometimes they occur in varying degrees of combination giving a unique appearance on the imaging studies. We describe a case of neur...

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Detalles Bibliográficos
Autores principales: Singhal, Namit, Agarwal, Sunil
Formato: Texto
Lenguaje:English
Publicado: Medknow Publications 2010
Materias:
Neuroimaging
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3087987/
https://www.ncbi.nlm.nih.gov/pubmed/21559156
http://dx.doi.org/10.4103/1817-1745.76106
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author Singhal, Namit
Agarwal, Sunil
author_facet Singhal, Namit
Agarwal, Sunil
author_sort Singhal, Namit
collection PubMed
description Developmental malformations of the cortex in neuronal migration disorders result in constellation of findings on radiological scanning. Isolated defects are common but sometimes they occur in varying degrees of combination giving a unique appearance on the imaging studies. We describe a case of neuronal migration disorder in which the computed tomography scan showed the presence of lissencephaly, colpocephaly. and Septal agenesis. These findings make the ventricular system appear in shape of a crown, which we refer to as “CROWN SIGN”, first described in neurosurgical literature..
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spelling pubmed-30879872011-05-10 Septal agenesis and lissencephaly with colpocephaly presenting as the ‘Crown Sign’ Singhal, Namit Agarwal, Sunil J Pediatr Neurosci Neuroimaging Developmental malformations of the cortex in neuronal migration disorders result in constellation of findings on radiological scanning. Isolated defects are common but sometimes they occur in varying degrees of combination giving a unique appearance on the imaging studies. We describe a case of neuronal migration disorder in which the computed tomography scan showed the presence of lissencephaly, colpocephaly. and Septal agenesis. These findings make the ventricular system appear in shape of a crown, which we refer to as “CROWN SIGN”, first described in neurosurgical literature.. Medknow Publications 2010 /pmc/articles/PMC3087987/ /pubmed/21559156 http://dx.doi.org/10.4103/1817-1745.76106 Text en © Journal of Pediatric Neurosciences http://creativecommons.org/licenses/by/2.0/ This is an open-access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Neuroimaging
Singhal, Namit
Agarwal, Sunil
Septal agenesis and lissencephaly with colpocephaly presenting as the ‘Crown Sign’
title Septal agenesis and lissencephaly with colpocephaly presenting as the ‘Crown Sign’
title_full Septal agenesis and lissencephaly with colpocephaly presenting as the ‘Crown Sign’
title_fullStr Septal agenesis and lissencephaly with colpocephaly presenting as the ‘Crown Sign’
title_full_unstemmed Septal agenesis and lissencephaly with colpocephaly presenting as the ‘Crown Sign’
title_short Septal agenesis and lissencephaly with colpocephaly presenting as the ‘Crown Sign’
title_sort septal agenesis and lissencephaly with colpocephaly presenting as the ‘crown sign’
topic Neuroimaging
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3087987/
https://www.ncbi.nlm.nih.gov/pubmed/21559156
http://dx.doi.org/10.4103/1817-1745.76106
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