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Motor Unit Abnormalities in Dystonia musculorum Mice
Dystonia musculorum (dt) is a mouse inherited sensory neuropathy caused by mutations in the dystonin gene. While the primary pathology lies in the sensory neurons of dt mice, the overt movement disorder suggests motor neurons may also be affected. Here, we report on the contribution of motor neurons...
Autores principales: | De Repentigny, Yves, Ferrier, Andrew, Ryan, Scott D., Sato, Tadasu, Kothary, Rashmi |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Public Library of Science
2011
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3115977/ https://www.ncbi.nlm.nih.gov/pubmed/21698255 http://dx.doi.org/10.1371/journal.pone.0021093 |
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