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Synergistic convergence and split pons in horizontal gaze palsy and progressive scoliosis in two sisters

Synergistic convergence is an ocular motor anomaly where on attempted abduction or on attempted horizontal gaze, both the eyes converge. It has been related to peripheral causes such as congenital fibrosis of extraocular muscles (CFEOM), congenital cranial dysinnervation syndrome, ocular misinnervat...

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Autores principales: Jain, Nitin R, Jethani, Jitendra, Narendran, Kalpana, Kanth, L
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications 2011
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3116551/
https://www.ncbi.nlm.nih.gov/pubmed/21350292
http://dx.doi.org/10.4103/0301-4738.77012
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author Jain, Nitin R
Jethani, Jitendra
Narendran, Kalpana
Kanth, L
author_facet Jain, Nitin R
Jethani, Jitendra
Narendran, Kalpana
Kanth, L
author_sort Jain, Nitin R
collection PubMed
description Synergistic convergence is an ocular motor anomaly where on attempted abduction or on attempted horizontal gaze, both the eyes converge. It has been related to peripheral causes such as congenital fibrosis of extraocular muscles (CFEOM), congenital cranial dysinnervation syndrome, ocular misinnervation or rarely central causes like horizontal gaze palsy with progressive scoliosis, brain stem dysplasia. We hereby report the occurrence of synergistic convergence in two sisters. Both of them also had kyphoscoliosis. Magnetic resonance imaging (MRI) brain and spine in both the patients showed signs of brain stem dysplasia (split pons sign) differing in degree (younger sister had more marked changes).
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spelling pubmed-31165512011-06-21 Synergistic convergence and split pons in horizontal gaze palsy and progressive scoliosis in two sisters Jain, Nitin R Jethani, Jitendra Narendran, Kalpana Kanth, L Indian J Ophthalmol Brief Communications Synergistic convergence is an ocular motor anomaly where on attempted abduction or on attempted horizontal gaze, both the eyes converge. It has been related to peripheral causes such as congenital fibrosis of extraocular muscles (CFEOM), congenital cranial dysinnervation syndrome, ocular misinnervation or rarely central causes like horizontal gaze palsy with progressive scoliosis, brain stem dysplasia. We hereby report the occurrence of synergistic convergence in two sisters. Both of them also had kyphoscoliosis. Magnetic resonance imaging (MRI) brain and spine in both the patients showed signs of brain stem dysplasia (split pons sign) differing in degree (younger sister had more marked changes). Medknow Publications 2011 /pmc/articles/PMC3116551/ /pubmed/21350292 http://dx.doi.org/10.4103/0301-4738.77012 Text en © Indian Journal of Ophthalmology http://creativecommons.org/licenses/by/2.0/ This is an open-access article distributed under the terms of the Creative Commons Attribution Licence, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Brief Communications
Jain, Nitin R
Jethani, Jitendra
Narendran, Kalpana
Kanth, L
Synergistic convergence and split pons in horizontal gaze palsy and progressive scoliosis in two sisters
title Synergistic convergence and split pons in horizontal gaze palsy and progressive scoliosis in two sisters
title_full Synergistic convergence and split pons in horizontal gaze palsy and progressive scoliosis in two sisters
title_fullStr Synergistic convergence and split pons in horizontal gaze palsy and progressive scoliosis in two sisters
title_full_unstemmed Synergistic convergence and split pons in horizontal gaze palsy and progressive scoliosis in two sisters
title_short Synergistic convergence and split pons in horizontal gaze palsy and progressive scoliosis in two sisters
title_sort synergistic convergence and split pons in horizontal gaze palsy and progressive scoliosis in two sisters
topic Brief Communications
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3116551/
https://www.ncbi.nlm.nih.gov/pubmed/21350292
http://dx.doi.org/10.4103/0301-4738.77012
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