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Alterations of lipid metabolism in Wilson disease
INTRODUCTION: Wilson disease (WD) is an inherited disorder of human copper metabolism, characterised by accumulation of copper predominantly in the liver and brain, leading to severe hepatic and neurological disease. Interesting findings in animal models of WD (Atp7b(-/- )and LEC rats) showed altere...
Autores principales: | Seessle, Jessica, Gohdes, Annina, Gotthardt, Daniel Nils, Pfeiffenberger, Jan, Eckert, Nicola, Stremmel, Wolfgang, Reuner, Ulrike, Weiss, Karl Heinz |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
BioMed Central
2011
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3127787/ https://www.ncbi.nlm.nih.gov/pubmed/21595966 http://dx.doi.org/10.1186/1476-511X-10-83 |
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