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From glycosylation disorders to dolichol biosynthesis defects: a new class of metabolic diseases
Polyisoprenoid alcohols are membrane lipids that are present in every cell, conserved from archaea to higher eukaryotes. The most common form, alpha-saturated polyprenol or dolichol is present in all tissues and most organelle membranes of eukaryotic cells. Dolichol has a well defined role as a lipi...
Autores principales: | Cantagrel, Vincent, Lefeber, Dirk J. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Springer Netherlands
2011
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3137772/ https://www.ncbi.nlm.nih.gov/pubmed/21384228 http://dx.doi.org/10.1007/s10545-011-9301-0 |
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