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Anesthetic Management of a Pediatric Patient With Wilsons Disease
Wilsons disease, characterized by cirrhosis, extrapyramidal symptoms and Kayser-Fleischer corneal rings, is a rare hereditary disease of human copper metabolism. Clinical findings in Wilsons disease are complex and neurological symptoms such as tremor, dysarthria, rigid dystonia, seizures, psychiatr...
Autores principales: | , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
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Elmer Press
2010
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Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3140888/ https://www.ncbi.nlm.nih.gov/pubmed/21811529 http://dx.doi.org/10.4021/jocmr2010.04.292w |